Bioenergetics of mitochondrial diseases associated with mtDNA mutations

Biochimica et Biophysica Acta - Bioenergetics

Volumn 1658, Issue 1-2, 2004, Pages 89-94

  Lenaz, Giorgio ^a   Baracca, Alessandra ^a   Carelli, Valerio ^a   D'Aurelio, Marilena ^a   Sgarbi, Gianluca ^b   Solaini, Giancarlo ^b  

^a UNIVERSITY OF BOLOGNA   (Italy)

^b SCUOLA SUPERIORE SANT ANNA   (Italy)

Author keywords

ATP synthase; Complex I; Cytochrome oxidase subunit III; LHON; Mitochondrial cytopathy; NARP

Indexed keywords

ADENOSINE TRIPHOSPHATASE; ADENOSINE TRIPHOSPHATE; CYTOCHROME C OXIDASE; MITOCHONDRIAL DNA; REACTIVE OXYGEN METABOLITE;

BIOCHEMISTRY; BIOENERGY; CATALYSIS; CYBRID; DISEASE COURSE; DISORDERS OF MITOCHONDRIAL FUNCTIONS; GENE MUTATION; GENETIC ANALYSIS; HUMAN; HYDROLYSIS; LEBER HEREDITARY OPTIC NEUROPATHY; MELAS SYNDROME; MITOCHONDRIAL RESPIRATION; MOLECULAR GENETICS; NARP SYNDROME; PHENOTYPE; POINT MUTATION; PRIORITY JOURNAL; PROTEIN FUNCTION; PROTON TRANSPORT; REVIEW;

ADENOSINE TRIPHOSPHATASES; ANIMALS; ATAXIA; DNA, MITOCHONDRIAL; ELECTRON TRANSPORT COMPLEX IV; ENERGY METABOLISM; HUMANS; MELAS SYNDROME; MITOCHONDRIAL DISEASES; OPTIC NERVE DISEASES; POINT MUTATION; REACTIVE OXYGEN SPECIES; RETINITIS PIGMENTOSA; SYNDROME;

ATAXIA;

EID: 3543045616     PISSN: 00052728     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.bbabio.2004.03.013     Document Type: Review

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