Medium-term survival without haematopoietic stem cell transplantation in a case of IPEX: Insights into nutritional and immunosuppressive therapy

European Journal of Pediatrics

Volumn 166, Issue 11, 2007, Pages 1195-1197

  Taddio, Andrea ^a   Faleschini, Elena ^a   Valencic, Erica ^a   Granzotto, Marilena ^a   Tommasini, Alberto ^a,b   Lepore, Loredana ^b   Andolina, Marino ^b   Barbi, Egidio ^b   Ventura, Alessandro ^a,b  

^a UNIVERSITY OF TRIESTE   (Italy)

^b INSTITUTE FOR MATERNAL AND CHILD HEALTH IRCCS BURLO GAROFOLO   (Italy)

Author keywords

Autoimmunity; Immunodeficiency; IPEX; Treatment

Indexed keywords

BETAMETHASONE; CYCLOPHOSPHAMIDE; CYCLOSPORIN A; FLUDARABINE; GANCICLOVIR; GROWTH HORMONE; IMMUNOGLOBULIN; INSULIN; METHOTREXATE; PREDNISONE; RAPAMYCIN; RITUXIMAB; TACROLIMUS; VINCRISTINE;

ANTIBIOTIC THERAPY; ARTICLE; CASE REPORT; COMBINED IMMUNODEFICIENCY; CUSHING DISEASE; CYTOMEGALOVIRUS; DIARRHEA; DRUG DOSE REDUCTION; DRUG POTENCY; ECZEMA; GLYCEMIC CONTROL; HEMATOPOIETIC STEM CELL TRANSPLANTATION; HUMAN; IMMUNOSUPPRESSIVE TREATMENT; INSULIN PUMP; IPEX SYNDROME; LYMPHOCYTE TRANSFUSION; MALE; PARENT; PNEUMOCYSTIS PNEUMONIA; PNEUMONIA; PRESCHOOL CHILD; PRIORITY JOURNAL; SHORT COURSE THERAPY; STEROID THERAPY; SURVIVAL; TOTAL PARENTERAL NUTRITION; TREATMENT REFUSAL; WEIGHT REDUCTION;

ANTI-BACTERIAL AGENTS; AUTOIMMUNE DISEASES; COMBINED MODALITY THERAPY; FORKHEAD TRANSCRIPTION FACTORS; HUMANS; IMMUNOSUPPRESSIVE AGENTS; INFANT; MALE; NUTRITIONAL SUPPORT; STEROIDS;

EID: 34748915728     PISSN: 03406199     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00431-006-0395-6     Document Type: Article

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