β-Liddle mutation of the epithelial sodium channel increases alveolar fluid clearance and reduces the severity of hydrostatic pulmonary oedema in mice

Journal of Physiology

Volumn 582, Issue 2, 2007, Pages 777-788

  Randrianarison, Nadia ^a,b   Escoubet, Brigitte ^b,c   Ferreira, Chrystophe ^b   Fontayne, Alexandre ^a,b   Fowler Jaeger, Nicole ^d   Clerici, Christine ^a,b   Hummler, Edith ^d   Rossier, Bernard C ^d   Planès, Carole ^a,e  

^a CENTRE DE RECHERCHE BIOMÉDICALE BICHAT BEAUJON CRB3   (France)

^b UNIVERSITÉ PARIS DESCARTES   (France)

^c INSERM   (France)

^d UNIVERSITY OF LAUSANNE   (Switzerland)

^e LABORATOIRE DES SCIENCES DU CLIMAT ET DE L ENVIRONNEMENT   (France)

Author keywords

[No Author keywords available]

Indexed keywords

AMILORIDE; GENE PRODUCT; PROTEIN SCNN1B; SODIUM CHANNEL; TERBUTALINE; UNCLASSIFIED DRUG; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; EPITHELIAL SODIUM CHANNEL;

ANIMAL CELL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; DISEASE SEVERITY; ECHOCARDIOGRAPHY; GENE MUTATION; HEART FUNCTION; HETEROZYGOSITY; HOMOZYGOSITY; LUNG ALVEOLUS; LUNG ALVEOLUS EPITHELIUM; LUNG EDEMA; LUNG FLUID; LUNG VOLUME; LUNG WEIGHT; MOUSE; MOUSE STRAIN; NONHUMAN; PRIORITY JOURNAL; SODIUM TRANSPORT; WILD TYPE; ALVEOLAR FLUID CLEARANCE; ANIMAL EXPERIMENT; ANIMAL MODEL; CHANNEL GATING; EPITHELIAL LINING FLUID; FLUID BALANCE; GAIN OF FUNCTION MUTATION; GENE; HETEROZYGOTE; HOMOZYGOTE; LIDDLE SYNDROME; LUNG ALVEOLUS EPITHELIUM CELL; LUNG CLEARANCE; SCNN1B GENE;

EID: 34447267450     PISSN: 00223751     EISSN: 14697793     Source Type: Journal    
DOI: 10.1113/jphysiol.2007.131078     Document Type: Article

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