Pathophysiology of cystic fibrosis

Annales Nestle

Volumn 64, Issue 3, 2006, Pages 101-109

  Donaldson, Scott H ^a,b   Boucher, Richard C ^a  

^a UNIVERSITY OF NORTH CAROLINA SCHOOL OF MEDICINE   (United States)

^b UNIVERSITY OF NORTH CAROLINA   (United States)

Author keywords

Airway surface liquid; CFTR; Cystic fibrosis; Epithelial sodium channel; Ion transport; Mucus clearance

Indexed keywords

ANTIBIOTIC AGENT; TRANSMEMBRANE CONDUCTANCE REGULATOR;

AIRWAY; BACTERIAL INFECTION; BRONCHIECTASIS; CYSTIC FIBROSIS; DEFENSE MECHANISM; DEHYDRATION; DISEASE COURSE; ELECTROLYTE TRANSPORT; EPITHELIUM CELL; HOST RESISTANCE; HUMAN; INFLAMMATION; INNATE IMMUNITY; ION TRANSPORT; LUNG CLEARANCE; LUNG DISEASE; LUNG INJURY; MOLECULAR CLONING; NEUTROPHIL; PATHOPHYSIOLOGY; RESPIRATORY FAILURE; REVIEW; WATER TRANSPORT;

EID: 33751110259     PISSN: 05178606     EISSN: 16614011     Source Type: Journal    
DOI: 10.1159/000095374     Document Type: Review

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