-
1
-
-
0002977005
-
Maple syrup urine disease (branched-chain ketoaciduria)
-
8th edition C.R. Scriver A.L. Beaudet W.S. Sly D. Valle McGraw-Hill New York
-
D.T. Chuang, and V.E. Shih Maple syrup urine disease (branched-chain ketoaciduria) 8th edition C.R. Scriver A.L. Beaudet W.S. Sly D. Valle The metabolic and molecular bases of inherited disease vol. 2 2001 McGraw-Hill New York 1971 2005
-
(2001)
The Metabolic and Molecular Bases of Inherited Disease
, vol.2
, pp. 1971-2005
-
-
Chuang, D.T.1
Shih, V.E.2
-
2
-
-
0000299656
-
Disorders of branched-chain amino acid and ketoacid metabolism
-
C.R. Scriver A.L. Beaudet W.S. Sly D. Valle 6th edition McGraw-Hill New York
-
D.J. Danner, and L.J. Elsas Disorders of branched-chain amino acid and ketoacid metabolism C.R. Scriver A.L. Beaudet W.S. Sly D. Valle The metabolic basis of inherited disease 6th edition 1989 McGraw-Hill New York 671 692
-
(1989)
The Metabolic Basis of Inherited Disease
, pp. 671-692
-
-
Danner, D.J.1
Elsas, L.J.2
-
3
-
-
0001760204
-
Maple syrup urine disease, with particular reference to dietotherapy
-
S.E. Snyderman, P.M. Norton, E. Roitman, and L.E. Holt Jr. Maple syrup urine disease, with particular reference to dietotherapy Pediatrics 34 1964 454 472
-
(1964)
Pediatrics
, vol.34
, pp. 454-472
-
-
Snyderman, S.E.1
Norton, P.M.2
Roitman, E.3
Holt Jr., L.E.4
-
4
-
-
0000130718
-
Aminoaciduria
-
M.L. Efron Aminoaciduria N Engl J Med 272 1965 1058 1067
-
(1965)
N Engl J Med
, vol.272
, pp. 1058-1067
-
-
Efron, M.L.1
-
5
-
-
0033575298
-
Chronic early leucine administration induces behavioral deficits in rats
-
C.F. Mello, L. Feksa, A.M. Brusque, C.M. Wannmacher, and M. Wajner Chronic early leucine administration induces behavioral deficits in rats Life Sci 65 1999 747 755
-
(1999)
Life Sci
, vol.65
, pp. 747-755
-
-
Mello, C.F.1
Feksa, L.2
Brusque, A.M.3
Wannmacher, C.M.4
Wajner, M.5
-
6
-
-
0346023961
-
Intrahippocampal administration of the α-keto acids accumulating in maple syrup urine disease provokes learning deficits in rats
-
V. de Castro Vasques, M.A. Boer, F. Diligenti, F. Brinco, F. Mallman, and C.F. Mello Intrahippocampal administration of the α-keto acids accumulating in maple syrup urine disease provokes learning deficits in rats Pharmacol Biochem Behav 77 2004 183 190
-
(2004)
Pharmacol Biochem Behav
, vol.77
, pp. 183-190
-
-
De Castro Vasques, V.1
Boer, M.A.2
Diligenti, F.3
Brinco, F.4
Mallman, F.5
Mello, C.F.6
-
7
-
-
0035831068
-
Pharmacological evidence that alpha-ketoisovaleric acid induces convulsions through GABAergic and glutamatergic mechanisms in rats
-
A.S. Coitinho, C.F. de Mello, T.T. Lima, J. de Bastiani, M.R. Fighera, and M. Wajner Pharmacological evidence that alpha-ketoisovaleric acid induces convulsions through GABAergic and glutamatergic mechanisms in rats Brain Res 894 2001 68 73
-
(2001)
Brain Res
, vol.894
, pp. 68-73
-
-
Coitinho, A.S.1
De Mello, C.F.2
Lima, T.T.3
De Bastiani, J.4
Fighera, M.R.5
Wajner, M.6
-
8
-
-
0001234745
-
Influence of α-keto acids on the respiration of brain in vitro
-
R.K. Howell, and M. Lee Influence of α-keto acids on the respiration of brain in vitro Proc Soc Exp Biol Med 113 1963 660 663
-
(1963)
Proc Soc Exp Biol Med
, vol.113
, pp. 660-663
-
-
Howell, R.K.1
Lee, M.2
-
9
-
-
0016259467
-
Inhibition of mitochondrial pyruvate transport by phenylpyruvate and alpha-ketoisocaproate
-
A.P. Halestrap, M.D. Brand, and R.M. Denton Inhibition of mitochondrial pyruvate transport by phenylpyruvate and alpha-ketoisocaproate Biochim Biophys Acta 367 1974 102 108
-
(1974)
Biochim Biophys Acta
, vol.367
, pp. 102-108
-
-
Halestrap, A.P.1
Brand, M.D.2
Denton, R.M.3
-
10
-
-
0017258183
-
Control of pyruvate and beta-hydroxy-butyrate utilization in rat brain mitochondria and its relevance to phenylketonuria and maple syrup urine disease
-
J.M. Land, J. Mowbray, and J.B. Clark Control of pyruvate and beta-hydroxy-butyrate utilization in rat brain mitochondria and its relevance to phenylketonuria and maple syrup urine disease J Neurochem 26 1976 823 830
-
(1976)
J Neurochem
, vol.26
, pp. 823-830
-
-
Land, J.M.1
Mowbray, J.2
Clark, J.B.3
-
11
-
-
0037403502
-
Creatine kinase activity from rat brain is inhibited by branched-chain amino acids in vitro
-
C. Pilla, R.F. Cardozo, C.S. Dutra-Filho, A.T. Wyse, M. Wajner, and C.M. Wannmacher Creatine kinase activity from rat brain is inhibited by branched-chain amino acids in vitro Neurochem Res 28 2003 675 679
-
(2003)
Neurochem Res
, vol.28
, pp. 675-679
-
-
Pilla, C.1
Cardozo, R.F.2
Dutra-Filho, C.S.3
Wyse, A.T.4
Wajner, M.5
Wannmacher, C.M.6
-
12
-
-
0242543265
-
Inhibition of brain energy metabolism by the alpha-keto acids accumulating in maple syrup urine disease
-
A.M. Sgaravatti, R.B. Rosa, P.F. Schuck, C.A. Ribeiro, C.M. Wannmacher, and A.T. Wyse Inhibition of brain energy metabolism by the alpha-keto acids accumulating in maple syrup urine disease Biochim Biophys Acta 1639 2003 232 238
-
(2003)
Biochim Biophys Acta
, vol.1639
, pp. 232-238
-
-
Sgaravatti, A.M.1
Rosa, R.B.2
Schuck, P.F.3
Ribeiro, C.A.4
Wannmacher, C.M.5
Wyse, A.T.6
-
13
-
-
0000819855
-
Inhibition of brain-glutamic decarboxylase by phenylalanine, valine, and leucine derivatives: A suggestion concerning the etiology of the neurological defect in phenylketonuria and branched-chain ketonuria
-
R.E. Tashian Inhibition of brain-glutamic decarboxylase by phenylalanine, valine, and leucine derivatives: a suggestion concerning the etiology of the neurological defect in phenylketonuria and branched-chain ketonuria Metabolism 10 1961 393 402
-
(1961)
Metabolism
, vol.10
, pp. 393-402
-
-
Tashian, R.E.1
-
14
-
-
0013966190
-
Inhibition of brain protein synthesis: An approach to a biochemical basis of neurological dysfunction in the amino-acidurias
-
S.H. Appel Inhibition of brain protein synthesis: an approach to a biochemical basis of neurological dysfunction in the amino-acidurias Trans N Y Acad Sci 29 1966 63 70
-
(1966)
Trans N Y Acad Sci
, vol.29
, pp. 63-70
-
-
Appel, S.H.1
-
15
-
-
0020606605
-
Abnormal protein and lipidic composition of the cerebral myelin of a patient with maple syrup urine disease
-
T. Taketomi, T. Kunishita, A. Hara, and S. Mizushima Abnormal protein and lipidic composition of the cerebral myelin of a patient with maple syrup urine disease Jpn J Exp Med 53 1983 109 116
-
(1983)
Jpn J Exp Med
, vol.53
, pp. 109-116
-
-
Taketomi, T.1
Kunishita, T.2
Hara, A.3
Mizushima, S.4
-
16
-
-
0020552907
-
Myelin proteins: Degradation in rat brain initiated by metabolites causative of maple syrup urine disease
-
D. Tribble, and R. Shapira Myelin proteins: degradation in rat brain initiated by metabolites causative of maple syrup urine disease Biochem Biophys Res Commun 114 1983 440 446
-
(1983)
Biochem Biophys Res Commun
, vol.114
, pp. 440-446
-
-
Tribble, D.1
Shapira, R.2
-
17
-
-
0026553444
-
Maple syrup urine disease: Interrelations between branched-chain amino-, oxo- and hydroxyacids; Implications for treatment; Associations with CNS dysmyelination
-
E. Treacy, C.L. Clow, T.R. Reade, D. Chitayat, O.A. Mamer, and C.R. Scriver Maple syrup urine disease: interrelations between branched-chain amino-, oxo- and hydroxyacids; implications for treatment; associations with CNS dysmyelination J Inherit Metab Dis 15 1992 121 135
-
(1992)
J Inherit Metab Dis
, vol.15
, pp. 121-135
-
-
Treacy, E.1
Clow, C.L.2
Reade, T.R.3
Chitayat, D.4
Mamer, O.A.5
Scriver, C.R.6
-
18
-
-
0032989964
-
Reduction of plasma concentrations of large neutral amino acids in patients with maple urine disease during crises
-
M. Wajner, and C.R. Vargas Reduction of plasma concentrations of large neutral amino acids in patients with maple urine disease during crises Arch Dis Child 80 1999 579
-
(1999)
Arch Dis Child
, vol.80
, pp. 579
-
-
Wajner, M.1
Vargas, C.R.2
-
19
-
-
0033913801
-
Reduction of large neutral amino acid concentration in plasma and CSF of patients with maple syrup urine disease during crises
-
M. Wajner, D.M. Coelho, A.G. Barschak, P.R. Araújo, R.F. Pires, and F.L. Lulhier Reduction of large neutral amino acid concentration in plasma and CSF of patients with maple syrup urine disease during crises J Inherit Metab Dis 23 2000 505 512
-
(2000)
J Inherit Metab Dis
, vol.23
, pp. 505-512
-
-
Wajner, M.1
Coelho, D.M.2
Barschak, A.G.3
Araújo, P.R.4
Pires, R.F.5
Lulhier, F.L.6
-
20
-
-
0035102870
-
Reduction of large neutral amino acid levels in plasma and brain of hyperleucinemic rats
-
P. Araujo, G.F. Wassermann, K. Tallini, V. Furlanetto, C.R. Vargas, and C.M. Wannmacher Reduction of large neutral amino acid levels in plasma and brain of hyperleucinemic rats Neurochem Int 38 2001 529 537
-
(2001)
Neurochem Int
, vol.38
, pp. 529-537
-
-
Araujo, P.1
Wassermann, G.F.2
Tallini, K.3
Furlanetto, V.4
Vargas, C.R.5
Wannmacher, C.M.6
-
21
-
-
0034108632
-
Branched chain amino acids induce apoptosis in neural cells without mitochondrial membrane depolarization or cytochrome c release: Implications for neurological impairment associated with maple syrup urine disease
-
P. Jouvet, P. Rustin, D.L. Taylor, J.M. Pocock, U. Felderhoff-Mueser, and N.D. Mazarakis Branched chain amino acids induce apoptosis in neural cells without mitochondrial membrane depolarization or cytochrome c release: implications for neurological impairment associated with maple syrup urine disease Mol Biol Cell 11 2000 1919 1932
-
(2000)
Mol Biol Cell
, vol.11
, pp. 1919-1932
-
-
Jouvet, P.1
Rustin, P.2
Taylor, D.L.3
Pocock, J.M.4
Felderhoff-Mueser, U.5
Mazarakis, N.D.6
-
22
-
-
0031282249
-
Memory formation: The sequence of biochemical events in the hippocampus and its connection to activity in other brain structures
-
I. Izquierdo, and J.H. Medina Memory formation: the sequence of biochemical events in the hippocampus and its connection to activity in other brain structures Neurobiol Learn Mem 68 1997 285 316
-
(1997)
Neurobiol Learn Mem
, vol.68
, pp. 285-316
-
-
Izquierdo, I.1
Medina, J.H.2
-
23
-
-
0034849061
-
Characteristics of hippocampal glycine release in cell-damaging conditions in the adult and developing mouse
-
P. Saransaari, and S.S. Oja Characteristics of hippocampal glycine release in cell-damaging conditions in the adult and developing mouse Neurochem Res 26 2001 845 852
-
(2001)
Neurochem Res
, vol.26
, pp. 845-852
-
-
Saransaari, P.1
Oja, S.S.2
-
24
-
-
0032746966
-
Open field motor patterns and object marking, but not object sniffing, are altered by ibotenate lesions of the hippocampus
-
C.W. Harley, and G.M. Martin Open field motor patterns and object marking, but not object sniffing, are altered by ibotenate lesions of the hippocampus Neurobiol Learn Mem 72 1999 202 204
-
(1999)
Neurobiol Learn Mem
, vol.72
, pp. 202-204
-
-
Harley, C.W.1
Martin, G.M.2
-
25
-
-
0037107023
-
Differential involvement of amygdala and hippocampus in responding to novel objects and contexts
-
S.N. Moses, R.J. Sutherland, and R.J. McDonald Differential involvement of amygdala and hippocampus in responding to novel objects and contexts Brain Res Bull 58 2002 517 527
-
(2002)
Brain Res Bull
, vol.58
, pp. 517-527
-
-
Moses, S.N.1
Sutherland, R.J.2
McDonald, R.J.3
-
26
-
-
0033988682
-
Amygdala, hippocampus and descriminative fear conditioning to context
-
E.A. Antoniadis, and R.J. McDonald Amygdala, hippocampus and descriminative fear conditioning to context Behav Brain Res 108 2000 1 19
-
(2000)
Behav Brain Res
, vol.108
, pp. 1-19
-
-
Antoniadis, E.A.1
McDonald, R.J.2
-
27
-
-
0034058460
-
Contextual fear, gestalt memories and the hippocampus
-
M.S. Fanselow Contextual fear, gestalt memories and the hippocampus Behav Brain Res 110 2000 73 81
-
(2000)
Behav Brain Res
, vol.110
, pp. 73-81
-
-
Fanselow, M.S.1
-
29
-
-
0032826620
-
Novelty causes time-dependent retrograde amnesia for one-trial avoidance in rats through NMDA receptor and CaMKII-dependent mechanisms in the hippocampus
-
I. Izquierdo, N. Schroder, C.A. Netto, and J.H. Medina Novelty causes time-dependent retrograde amnesia for one-trial avoidance in rats through NMDA receptor and CaMKII-dependent mechanisms in the hippocampus Eur J Neurosci 11 1999 3323 3328
-
(1999)
Eur J Neurosci
, vol.11
, pp. 3323-3328
-
-
Izquierdo, I.1
Schroder, N.2
Netto, C.A.3
Medina, J.H.4
-
30
-
-
0034660025
-
Different hippocampal molecular requirements for short- and long-term retrieval of one-trial avoidance learning
-
L.A. Izquierdo, D.M. Barros, P.G. Ardenghi, P. Pereira, C. Rodrigues, and H. Choi Different hippocampal molecular requirements for short- and long-term retrieval of one-trial avoidance learning Behav Brain Res 111 2000 93 98
-
(2000)
Behav Brain Res
, vol.111
, pp. 93-98
-
-
Izquierdo, L.A.1
Barros, D.M.2
Ardenghi, P.G.3
Pereira, P.4
Rodrigues, C.5
Choi, H.6
-
31
-
-
0000650706
-
The open-field test: A critical review
-
R.N. Walsh, and R.A. Cummins The open-field test: a critical review Psychol Bull 83 1976 482 504
-
(1976)
Psychol Bull
, vol.83
, pp. 482-504
-
-
Walsh, R.N.1
Cummins, R.A.2
-
32
-
-
0015837338
-
Tests for emotionality in rats and mice: A review
-
J. Archer Tests for emotionality in rats and mice: a review Anim Behav 21 1973 205 235
-
(1973)
Anim Behav
, vol.21
, pp. 205-235
-
-
Archer, J.1
-
33
-
-
0016781992
-
Emotionality, exploratory behavior and locomotion in aging inbred strains of mice
-
P.K. Elias, M.F. Elias, and B.E. Eleftheriou Emotionality, exploratory behavior and locomotion in aging inbred strains of mice Gerontologia 21 1975 46 55
-
(1975)
Gerontologia
, vol.21
, pp. 46-55
-
-
Elias, P.K.1
Elias, M.F.2
Eleftheriou, B.E.3
-
34
-
-
0014276169
-
Studies of exploratory behaviour in the albino rat
-
A.M. Walden Studies of exploratory behaviour in the albino rat Psychol. Rep. 22 1968 483 493
-
(1968)
Psychol. Rep.
, vol.22
, pp. 483-493
-
-
Walden, A.M.1
-
35
-
-
0022838252
-
Differential effect of post-training naloxone, beta-endorphin, leu-enkephalin and electroconvulsive shock administration upon memory of an open-field habituation and of a water-finding task
-
C.A. Netto, R.D. Dias, and I. Izquierdo Differential effect of post-training naloxone, beta-endorphin, leu-enkephalin and electroconvulsive shock administration upon memory of an open-field habituation and of a water-finding task Psychoneuroendocrinology 11 1986 437 446
-
(1986)
Psychoneuroendocrinology
, vol.11
, pp. 437-446
-
-
Netto, C.A.1
Dias, R.D.2
Izquierdo, I.3
-
36
-
-
0034283285
-
Molecular signalling pathways in the cerebral cortex are required for retrieval of one-trial avoidance learning in rats
-
D.M. Barros, L.A. Izquierdo, T. Mello e Souza, P.G. Ardenghi, P. Pereira, and J.H. Medina Molecular signalling pathways in the cerebral cortex are required for retrieval of one-trial avoidance learning in rats Behav Brain Res 114 2000 183 192
-
(2000)
Behav Brain Res
, vol.114
, pp. 183-192
-
-
Barros, D.M.1
Izquierdo, L.A.2
Mello Souza, E.T.3
Ardenghi, P.G.4
Pereira, P.5
Medina, J.H.6
-
37
-
-
0034626947
-
Alpha-ketoisocaproate increases the in vitro 32P incorporation into intermediate filaments in cerebral cortex of rats
-
T. Branco, R. Meirelles, B.B. da Rocha, A. de Mattos-Dutra, M. Wajner, and R. Pessoa-Pureur Alpha-ketoisocaproate increases the in vitro 32P incorporation into intermediate filaments in cerebral cortex of rats NeuroReport 11 2000 3545 3550
-
(2000)
NeuroReport
, vol.11
, pp. 3545-3550
-
-
Branco, T.1
Meirelles, R.2
Da Rocha, B.B.3
De Mattos-Dutra, A.4
Wajner, M.5
Pessoa-Pureur, R.6
-
38
-
-
0035987827
-
Effect of the branched-chain alpha-ketoacids accumulating in maple syrup urine disease on the high molecular weight neurofilament subunit (NF-H) in rat cerebral cortex
-
R. Pessoa-Pureur, C. Funchal, P. de Lima Pelaez, L. Vivian, S. Oliveira Loureiro, and R. de Freitas Miranda Effect of the branched-chain alpha-ketoacids accumulating in maple syrup urine disease on the high molecular weight neurofilament subunit (NF-H) in rat cerebral cortex Metab Brain Dis 17 2002 65 75
-
(2002)
Metab Brain Dis
, vol.17
, pp. 65-75
-
-
Pessoa-Pureur, R.1
Funchal, C.2
De Lima Pelaez, P.3
Vivian, L.4
Oliveira Loureiro, S.5
De Freitas Miranda, R.6
-
39
-
-
0037115295
-
Alpha-ketoisocaproic acid regulates phosphorylation of intermediate filaments in postnatal rat cortical slices through ionotropic glutamatergic receptors
-
C. Funchal, P. de Lima Pelaez, S.O. Loureiro, L. Vivian, F. Dall Bello Pessutto, and L.M. de Almeida Alpha-ketoisocaproic acid regulates phosphorylation of intermediate filaments in postnatal rat cortical slices through ionotropic glutamatergic receptors Brain Res Dev Brain Res 139 2002 267 276
-
(2002)
Brain Res Dev Brain Res
, vol.139
, pp. 267-276
-
-
Funchal, C.1
De Lima Pelaez, P.2
Loureiro, S.O.3
Vivian, L.4
Dall Bello Pessutto, F.5
De Almeida, L.M.6
-
40
-
-
0346219384
-
Alpha-keto-beta-methylvaleric acid increases the in vitro phosphorylation of intermediate filaments in cerebral cortex of young rats through the gabaergic system
-
C. Funchal, F. Dall Bello Pessutto, L.M. de Almeida, P. de Lima Pelaez, S.O. Loureiro, and L. Vivian Alpha-keto-beta-methylvaleric acid increases the in vitro phosphorylation of intermediate filaments in cerebral cortex of young rats through the gabaergic system J Neurol Sci 217 2004 17 24
-
(2004)
J Neurol Sci
, vol.217
, pp. 17-24
-
-
Funchal, C.1
Dall Bello Pessutto, F.2
De Almeida, L.M.3
De Lima Pelaez, P.4
Loureiro, S.O.5
Vivian, L.6
-
41
-
-
1842455649
-
Reduction of glutamate uptake into cerebral cortex of developing rats by the branched-chain alpha-keto acids accumulating in maple syrup urine disease
-
C. Funchal, A.M. Rosa, M. Wajner, S. Wofchuk, and R.P. Pureur Reduction of glutamate uptake into cerebral cortex of developing rats by the branched-chain alpha-keto acids accumulating in maple syrup urine disease Neurochem Res 29 2004 747 753
-
(2004)
Neurochem Res
, vol.29
, pp. 747-753
-
-
Funchal, C.1
Rosa, A.M.2
Wajner, M.3
Wofchuk, S.4
Pureur, R.P.5
-
42
-
-
0036186148
-
Stimulation of lipid peroxidation in vitro in rat brain by the metabolites accumulating in maple syrup urine disease
-
F.U. Fontella, E. Gassen, V. Pulronik, C.M. Wannmacher, A.B. Klein, and M. Wajner Stimulation of lipid peroxidation in vitro in rat brain by the metabolites accumulating in maple syrup urine disease Metab Brain Dis 17 2002 47 54
-
(2002)
Metab Brain Dis
, vol.17
, pp. 47-54
-
-
Fontella, F.U.1
Gassen, E.2
Pulronik, V.3
Wannmacher, C.M.4
Klein, A.B.5
Wajner, M.6
-
43
-
-
0018540819
-
Tuning out irrelevancy? Comments on Solomon's temporal mapping view of the hippocampus
-
J. O'Keefe, L. Nadel, and J. Willner Tuning out irrelevancy? Comments on Solomon's temporal mapping view of the hippocampus Psychol Bull 86 1979 1280 1289
-
(1979)
Psychol Bull
, vol.86
, pp. 1280-1289
-
-
O'Keefe, J.1
Nadel, L.2
Willner, J.3
-
44
-
-
0026691316
-
Object exploration and reactions to spatial and non spatial changes in hooded rats following damage to parietal cortex or hippocampal formation
-
E. Save, B. Poucet, N. Foreman, and M.C. Buhot Object exploration and reactions to spatial and non spatial changes in hooded rats following damage to parietal cortex or hippocampal formation Behav Neurosci 106 1992 447 456
-
(1992)
Behav Neurosci
, vol.106
, pp. 447-456
-
-
Save, E.1
Poucet, B.2
Foreman, N.3
Buhot, M.C.4
-
45
-
-
0028096701
-
Pharmacological evidence for a role of long-term potentiation in memory
-
I. Izquierdo Pharmacological evidence for a role of long-term potentiation in memory FASEB J 8 1994 1139 1145
-
(1994)
FASEB J
, vol.8
, pp. 1139-1145
-
-
Izquierdo, I.1
-
46
-
-
84984581025
-
Effect of perinatal lead exposure on rat behaviour in open-field and two-way avoidance tasks
-
A.L. Rodrigues, J.B. Rocha, C.F. Mello, and D.O. Souza Effect of perinatal lead exposure on rat behaviour in open-field and two-way avoidance tasks Pharmacol Toxicol 79 1996 150 156
-
(1996)
Pharmacol Toxicol
, vol.79
, pp. 150-156
-
-
Rodrigues, A.L.1
Rocha, J.B.2
Mello, C.F.3
Souza, D.O.4
-
47
-
-
0014695791
-
Open-field behavior in the rat: What does it mean?
-
V.H. Denenberg Open-field behavior in the rat: what does it mean? Ann NY Acad Sci 159 1969 852 859
-
(1969)
Ann NY Acad Sci
, vol.159
, pp. 852-859
-
-
Denenberg, V.H.1
-
48
-
-
0038268475
-
MR diffusion imaging and MR spectroscopy of maple syrup urine disease during acute metabolic decompensation
-
W. Jan, R.A. Zimmerman, Z.J. Wang, G.T. Berry, P.B. Kaplan, and E.M. Kaye MR diffusion imaging and MR spectroscopy of maple syrup urine disease during acute metabolic decompensation Neuroradiology 45 2003 393 399
-
(2003)
Neuroradiology
, vol.45
, pp. 393-399
-
-
Jan, W.1
Zimmerman, R.A.2
Wang, Z.J.3
Berry, G.T.4
Kaplan, P.B.5
Kaye, E.M.6
-
49
-
-
0038381516
-
Mitochondrial regulation of synaptic plasticity in the hippocampus
-
M. Levy, G.C. Faas, P. Saggau, W.J. Craigen, and D. Sweatt Mitochondrial regulation of synaptic plasticity in the hippocampus J Biol Chem 278 2003 17727 17734
-
(2003)
J Biol Chem
, vol.278
, pp. 17727-17734
-
-
Levy, M.1
Faas, G.C.2
Saggau, P.3
Craigen, W.J.4
Sweatt, D.5
-
50
-
-
0036351166
-
Noninvasive, in vivo approaches to evaluating behavior and exercise physiology in mouse models of mitochondrial disease
-
B.H. Graham, J.D. David Sweatt, and W.J. Craigen Noninvasive, in vivo approaches to evaluating behavior and exercise physiology in mouse models of mitochondrial disease Methods 26 2002 364 370
-
(2002)
Methods
, vol.26
, pp. 364-370
-
-
Graham, B.H.1
David Sweatt, J.D.2
Craigen, W.J.3
-
51
-
-
0142074341
-
Oral creatine monohydrate supplementation improves brain performance: A double-blind, placebo-controlled, cross-over trial
-
C. Rae, A.L. Digney, S.R. McEwan, and T.C. Bates Oral creatine monohydrate supplementation improves brain performance: a double-blind, placebo-controlled, cross-over trial Proc R Soc Lond, B Biol Sci 270 2003 2147 2150
-
(2003)
Proc R Soc Lond, B Biol Sci
, vol.270
, pp. 2147-2150
-
-
Rae, C.1
Digney, A.L.2
McEwan, S.R.3
Bates, T.C.4
-
52
-
-
0037129967
-
Health implications of creatine: Can oral creatine supplementation protect against neurological and atherosclerotic disease?
-
M. Wyss, and A. Schulze Health implications of creatine: can oral creatine supplementation protect against neurological and atherosclerotic disease? Neuroscience 112 2002 243 260
-
(2002)
Neuroscience
, vol.112
, pp. 243-260
-
-
Wyss, M.1
Schulze, A.2
-
53
-
-
0033935979
-
Creatine and creatinine metabolism
-
M. Wyss, and R. Kaddurah-Daouk Creatine and creatinine metabolism Physiol Rev 80 2000 1007 1213
-
(2000)
Physiol Rev
, vol.80
, pp. 1007-1213
-
-
Wyss, M.1
Kaddurah-Daouk, R.2
-
54
-
-
0016690789
-
The effect of succinic semialdehyde and sodium succinate on the higher nervous activity in normal subjects
-
J. Saarma, M. Saarma, A. Aadamsoo, K. Jatsa, J. Liivamagi, and L. Mehilane The effect of succinic semialdehyde and sodium succinate on the higher nervous activity in normal subjects Int Pharmacopsychiatry 10 1975 149 156
-
(1975)
Int Pharmacopsychiatry
, vol.10
, pp. 149-156
-
-
Saarma, J.1
Saarma, M.2
Aadamsoo, A.3
Jatsa, K.4
Liivamagi, J.5
Mehilane, L.6
-
55
-
-
0029893660
-
Intraestriatal methylmalonic acid administration induces rotational behavior and convulsions through glutamatergic mechanisms
-
C.F. de Mello, J. Begnini, R.E. Jimenez-Bernau, M.A. Rubin, B.J. de Astiani, and E. da Costa Jr. Intraestriatal methylmalonic acid administration induces rotational behavior and convulsions through glutamatergic mechanisms Brain Res 721 1996 120 125
-
(1996)
Brain Res
, vol.721
, pp. 120-125
-
-
De Mello, C.F.1
Begnini, J.2
Jimenez-Bernau, R.E.3
Rubin, M.A.4
De Astiani, B.J.5
Da Costa Jr., E.6
-
56
-
-
12444315618
-
Creatine protects against the convulsive behavior and lactate production elicited by the intrastriatal injection of methylmalonate
-
L.F. Royes, M.R. Fighera, A.F. Furian, M.S. Oliveira, L.G. da Silva, and C.R. Malfatti Creatine protects against the convulsive behavior and lactate production elicited by the intrastriatal injection of methylmalonate Neuroscience 118 2003 1079 1090
-
(2003)
Neuroscience
, vol.118
, pp. 1079-1090
-
-
Royes, L.F.1
Fighera, M.R.2
Furian, A.F.3
Oliveira, M.S.4
Da Silva, L.G.5
Malfatti, C.R.6
-
57
-
-
0021042770
-
Organic acids and branched-chain amino acids in body fluids before and after multiple exchange transfusions in maple syrup urine disease
-
Y. Shigematsu, K. Kikuchi, T. Momoi, M. Sudo, Y. Kikawa, and K. Nosaka Organic acids and branched-chain amino acids in body fluids before and after multiple exchange transfusions in maple syrup urine disease J Inherit Metab Dis 6 1983 183 189
-
(1983)
J Inherit Metab Dis
, vol.6
, pp. 183-189
-
-
Shigematsu, Y.1
Kikuchi, K.2
Momoi, T.3
Sudo, M.4
Kikawa, Y.5
Nosaka, K.6
-
58
-
-
0028999188
-
Selective vulnerability of the CA1 region of hippocampus to the indirect excitotoxic effects of malonic acid
-
C. Davolio, and J.T. Greenamyre Selective vulnerability of the CA1 region of hippocampus to the indirect excitotoxic effects of malonic acid Neurosci Lett 192 1995 29 32
-
(1995)
Neurosci Lett
, vol.192
, pp. 29-32
-
-
Davolio, C.1
Greenamyre, J.T.2
|