-
1
-
-
0002911516
-
Disorders of propionate and methylmalonate metabolism
-
Scriver C.R., Beaudet A.L., Sly W.S., and Valle D. (Eds), McGraw-Hill, New York
-
Fenton W.A., Gravel R.A., and Rosenblatt D.S. Disorders of propionate and methylmalonate metabolism. In: Scriver C.R., Beaudet A.L., Sly W.S., and Valle D. (Eds). The metabolic and molecular bases of inherited disease. 8th edition vol. 2 (2001), McGraw-Hill, New York 2165-2194
-
(2001)
The metabolic and molecular bases of inherited disease. 8th edition
, vol.2
, pp. 2165-2194
-
-
Fenton, W.A.1
Gravel, R.A.2
Rosenblatt, D.S.3
-
2
-
-
0027184507
-
Physiology and pathophysiology of organic acids in cerebrospinal fluid
-
Hoffmann G.F., Meier-Augenstein W., Stockler S., Surtees R., Rating D., and Nyhan W.L. Physiology and pathophysiology of organic acids in cerebrospinal fluid. J Inherit Metab Dis 16 (1993) 648-669
-
(1993)
J Inherit Metab Dis
, vol.16
, pp. 648-669
-
-
Hoffmann, G.F.1
Meier-Augenstein, W.2
Stockler, S.3
Surtees, R.4
Rating, D.5
Nyhan, W.L.6
-
3
-
-
0026568705
-
Effect of methylmalonate on in vitro lactate release and carbon dioxide production by brain suckling rats
-
Wajner M., Dutra J.C., Cardoso S.E., Wannmacher C.M., and Motta E.R. Effect of methylmalonate on in vitro lactate release and carbon dioxide production by brain suckling rats. J Inherit Metab Dis 15 (1992) 92-96
-
(1992)
J Inherit Metab Dis
, vol.15
, pp. 92-96
-
-
Wajner, M.1
Dutra, J.C.2
Cardoso, S.E.3
Wannmacher, C.M.4
Motta, E.R.5
-
4
-
-
0027510585
-
Inhibition of succinate dehydrogenase and betahydroxybutyrate dehydrogenase activities by methylmalonate in brain and liver of developing rats
-
Dutra J.C., Dutra-Filho C.S., Cardozo S.E., Wannmacher C.M., Sarkis J.J., and Wajner M. Inhibition of succinate dehydrogenase and betahydroxybutyrate dehydrogenase activities by methylmalonate in brain and liver of developing rats. J Inherit Metab Dis 1 (1993) 147-153
-
(1993)
J Inherit Metab Dis
, vol.1
, pp. 147-153
-
-
Dutra, J.C.1
Dutra-Filho, C.S.2
Cardozo, S.E.3
Wannmacher, C.M.4
Sarkis, J.J.5
Wajner, M.6
-
5
-
-
0028884492
-
Methylmalonic acid inhibits respiration in rat liver mitochondria
-
Toyoshima S., Watanabe F., Saido H., Miyatake K., and Nakano Y. Methylmalonic acid inhibits respiration in rat liver mitochondria. J Nutr 125 (1995) 2846-2850
-
(1995)
J Nutr
, vol.125
, pp. 2846-2850
-
-
Toyoshima, S.1
Watanabe, F.2
Saido, H.3
Miyatake, K.4
Nakano, Y.5
-
6
-
-
0030772253
-
Neurological dysfunction in methylmalonic acidaemia is probably related to the inhibitory effect of methylmalonate on brain energy production
-
Wajner M., and Coelho J.C. Neurological dysfunction in methylmalonic acidaemia is probably related to the inhibitory effect of methylmalonate on brain energy production. J Inherit Metab Dis 20 (1997) 761-768
-
(1997)
J Inherit Metab Dis
, vol.20
, pp. 761-768
-
-
Wajner, M.1
Coelho, J.C.2
-
7
-
-
0031841091
-
Methylmalonate toxicity in primary neuronal cultures
-
McLaughlin B.A., Nelson D., Silver I., Erescinska M., and Chesselet M.F. Methylmalonate toxicity in primary neuronal cultures. Neuroscience 86 (1998) 279-290
-
(1998)
Neuroscience
, vol.86
, pp. 279-290
-
-
McLaughlin, B.A.1
Nelson, D.2
Silver, I.3
Erescinska, M.4
Chesselet, M.F.5
-
8
-
-
0034647727
-
Methylmalonate administration decreases Na+, K+-ATPase activity in cerebral cortex of rats
-
Wyse A.T., Streck E.L., Barros S.V., Brusque A.M., Zugno A.I., and Wajner M. Methylmalonate administration decreases Na+, K+-ATPase activity in cerebral cortex of rats. Neuroreport 11 (2000) 2234-2331
-
(2000)
Neuroreport
, vol.11
, pp. 2234-2331
-
-
Wyse, A.T.1
Streck, E.L.2
Barros, S.V.3
Brusque, A.M.4
Zugno, A.I.5
Wajner, M.6
-
9
-
-
18344376530
-
Inhibition of the mitochondrial respiratory chain complex activities in rat cerebral cortex by methylmalonic acid
-
Brusque A.M., Borba Rosa R., Schuck P.F., Dalcin K.B., Ribeiro C.A., Silva C.G., et al. Inhibition of the mitochondrial respiratory chain complex activities in rat cerebral cortex by methylmalonic acid. Neurochem Int 40 (2002) 593-601
-
(2002)
Neurochem Int
, vol.40
, pp. 593-601
-
-
Brusque, A.M.1
Borba Rosa, R.2
Schuck, P.F.3
Dalcin, K.B.4
Ribeiro, C.A.5
Silva, C.G.6
-
10
-
-
12444315618
-
Creatine protects against the convulsive behavior and lactate production elicited by the intrastriatal injection of methylmalonate
-
Royes L.F., Fighera M.R., Furian A.F., Oliveira M.S., da Silva L.G., Malfatti C.R., et al. Creatine protects against the convulsive behavior and lactate production elicited by the intrastriatal injection of methylmalonate. Neuroscience 118 (2003) 1079-1090
-
(2003)
Neuroscience
, vol.118
, pp. 1079-1090
-
-
Royes, L.F.1
Fighera, M.R.2
Furian, A.F.3
Oliveira, M.S.4
da Silva, L.G.5
Malfatti, C.R.6
-
11
-
-
3042647320
-
Inhibition of mitochondrial creatine kinase activity from rat cerebral cortex by methylmalonic acid
-
Schuck P.F., Rosa R.B., Pettenuzzo L.F., Sitta A., Wannmacher C.M., Wyse A.T., et al. Inhibition of mitochondrial creatine kinase activity from rat cerebral cortex by methylmalonic acid. Neurochem Int 45 (2004) 661-667
-
(2004)
Neurochem Int
, vol.45
, pp. 661-667
-
-
Schuck, P.F.1
Rosa, R.B.2
Pettenuzzo, L.F.3
Sitta, A.4
Wannmacher, C.M.5
Wyse, A.T.6
-
13
-
-
0031282249
-
Memory formation: the sequence of biochemical events in the hippocampus and its connection to activity in other brain structures
-
Izquierdo I., and Medina J.H. Memory formation: the sequence of biochemical events in the hippocampus and its connection to activity in other brain structures. Neurobiol Learn Mem 68 (1997) 285-316
-
(1997)
Neurobiol Learn Mem
, vol.68
, pp. 285-316
-
-
Izquierdo, I.1
Medina, J.H.2
-
14
-
-
0032826620
-
Novelty causes time-dependent retrograde amnesia for one-trial avoidance in rats through NMDA receptor and CaMKII-dependent mechanisms in the hippocampus
-
Izquierdo I., Schroder N., Netto C.A., and Medina J.H. Novelty causes time-dependent retrograde amnesia for one-trial avoidance in rats through NMDA receptor and CaMKII-dependent mechanisms in the hippocampus. Eur J Neurosci 11 (1999) 3323-3328
-
(1999)
Eur J Neurosci
, vol.11
, pp. 3323-3328
-
-
Izquierdo, I.1
Schroder, N.2
Netto, C.A.3
Medina, J.H.4
-
15
-
-
0034660025
-
Different hippocampal molecular requirements for short- and long-term retrieval of one-trial avoidance learning
-
Izquierdo L.A., Barros D.M., Ardenghi P.G., Pereira P., Rodrigues C., Choi H., et al. Different hippocampal molecular requirements for short- and long-term retrieval of one-trial avoidance learning. Behav Brain Res 111 (2000) 93-98
-
(2000)
Behav Brain Res
, vol.111
, pp. 93-98
-
-
Izquierdo, L.A.1
Barros, D.M.2
Ardenghi, P.G.3
Pereira, P.4
Rodrigues, C.5
Choi, H.6
-
16
-
-
0000650706
-
The open-field test: a critical review
-
Walsh R.N., and Cummins R.A. The open-field test: a critical review. Psychol Bull 83 (1976) 482-504
-
(1976)
Psychol Bull
, vol.83
, pp. 482-504
-
-
Walsh, R.N.1
Cummins, R.A.2
-
17
-
-
0015837338
-
Tests for emotionality in rats and mice: a review
-
Archer J. Tests for emotionality in rats and mice: a review. Ann Behav 21 (1973) 205-235
-
(1973)
Ann Behav
, vol.21
, pp. 205-235
-
-
Archer, J.1
-
18
-
-
0016781992
-
Emotionality, exploratory behavior and locomotion in aging inbred strains of mice
-
Elias P.K., Elias M.F., and Eleftheriou B.E. Emotionality, exploratory behavior and locomotion in aging inbred strains of mice. Gerontologia 21 (1975) 46-55
-
(1975)
Gerontologia
, vol.21
, pp. 46-55
-
-
Elias, P.K.1
Elias, M.F.2
Eleftheriou, B.E.3
-
19
-
-
0014276169
-
Studies of exploratory behaviour in the albino rat
-
Walden A.M. Studies of exploratory behaviour in the albino rat. Psychol Reply 22 (1968) 483-493
-
(1968)
Psychol Reply
, vol.22
, pp. 483-493
-
-
Walden, A.M.1
-
20
-
-
0022838252
-
Differential effect of post-training naloxone, beta-endorphin, leu-enkephalin and electroconvulsive shock administration upon memory of an open-field habituation and of a water-finding task
-
Netto C.A., Dias R.D., and Izquierdo I. Differential effect of post-training naloxone, beta-endorphin, leu-enkephalin and electroconvulsive shock administration upon memory of an open-field habituation and of a water-finding task. Psychoneuroendocrinology 11 (1986) 437-446
-
(1986)
Psychoneuroendocrinology
, vol.11
, pp. 437-446
-
-
Netto, C.A.1
Dias, R.D.2
Izquierdo, I.3
-
21
-
-
0034283285
-
Molecular signalling pathways in the cerebral cortex are required for retrieval of one-trial avoidance learning in rats
-
Barros D.M., Izquierdo L.A., Mello e Souza T., Ardenghi P.G., Pereira P., Medina J.H., et al. Molecular signalling pathways in the cerebral cortex are required for retrieval of one-trial avoidance learning in rats. Behav Brain Res 114 (2000) 183-192
-
(2000)
Behav Brain Res
, vol.114
, pp. 183-192
-
-
Barros, D.M.1
Izquierdo, L.A.2
Mello e Souza, T.3
Ardenghi, P.G.4
Pereira, P.5
Medina, J.H.6
-
22
-
-
0029893660
-
Intrastriatal methylmalonic acid administration induces rotational behavior and convulsions through glutamatergic mechanisms
-
de Mello C.F., Begnini J., Jimenez-Bernal R.E., Rubin M.A., de Bastiani J., da Costa Jr. E., et al. Intrastriatal methylmalonic acid administration induces rotational behavior and convulsions through glutamatergic mechanisms. Brain Res 721 (1996) 120-125
-
(1996)
Brain Res
, vol.721
, pp. 120-125
-
-
de Mello, C.F.1
Begnini, J.2
Jimenez-Bernal, R.E.3
Rubin, M.A.4
de Bastiani, J.5
da Costa Jr., E.6
-
23
-
-
0347950966
-
The impact of screening for propionic and methylmalonic acidaemia
-
Leonard J.V., Vijayaraghavan S., and Walter J.H. The impact of screening for propionic and methylmalonic acidaemia. Eur J Pediatr 162 (2003) S21-S24
-
(2003)
Eur J Pediatr
, vol.162
-
-
Leonard, J.V.1
Vijayaraghavan, S.2
Walter, J.H.3
-
24
-
-
0014695791
-
Open-field behavior in the rat: what does it mean?
-
Denenberg V.H. Open-field behavior in the rat: what does it mean?. Ann N Y Acad Sci 159 (1969) 852-859
-
(1969)
Ann N Y Acad Sci
, vol.159
, pp. 852-859
-
-
Denenberg, V.H.1
-
25
-
-
0018540819
-
Tuning out irrelevancy? Comments on Solomon's temporal mapping view of the hippocampus
-
O'Keefe J., Nadel L., and Willner J. Tuning out irrelevancy? Comments on Solomon's temporal mapping view of the hippocampus. Psychol Bull 86 (1979) 1280-1289
-
(1979)
Psychol Bull
, vol.86
, pp. 1280-1289
-
-
O'Keefe, J.1
Nadel, L.2
Willner, J.3
-
26
-
-
0026691316
-
Object exploration and reactions to spatial and non spatial changes in hooded rats following damage to parietal cortex or hippocampal formation
-
Save E., Poucet B., Foreman N., and Buhot M.C. Object exploration and reactions to spatial and non spatial changes in hooded rats following damage to parietal cortex or hippocampal formation. Behav Neurosci 106 (1992) 447-456
-
(1992)
Behav Neurosci
, vol.106
, pp. 447-456
-
-
Save, E.1
Poucet, B.2
Foreman, N.3
Buhot, M.C.4
-
27
-
-
0028096701
-
Pharmacological evidence for a role of long-term potentiation in memory
-
Izquierdo I. Pharmacological evidence for a role of long-term potentiation in memory. FASEB J 8 (1994) 1139-1145
-
(1994)
FASEB J
, vol.8
, pp. 1139-1145
-
-
Izquierdo, I.1
-
28
-
-
84984581025
-
Effect of perinatal lead exposure on rat behaviour in open-field and two-way avoidance tasks
-
Rodrigues A.L., Rocha J.B., Mello C.F., and Souza D.O. Effect of perinatal lead exposure on rat behaviour in open-field and two-way avoidance tasks. Pharmacol Toxicol 79 (1996) 150-156
-
(1996)
Pharmacol Toxicol
, vol.79
, pp. 150-156
-
-
Rodrigues, A.L.1
Rocha, J.B.2
Mello, C.F.3
Souza, D.O.4
-
29
-
-
0032483521
-
Octamer formation and coupling of cardiac sarcomeric mitochondrial creatine kinase are mediated by charged N-terminal residues
-
Khuchua Z.A., Qin W., Boero J., Cheng J., Payne R.M., Saks V.A., et al. Octamer formation and coupling of cardiac sarcomeric mitochondrial creatine kinase are mediated by charged N-terminal residues. J Biol Chem 273 (1998) 22990-22996
-
(1998)
J Biol Chem
, vol.273
, pp. 22990-22996
-
-
Khuchua, Z.A.1
Qin, W.2
Boero, J.3
Cheng, J.4
Payne, R.M.5
Saks, V.A.6
-
30
-
-
0034625438
-
Octamers of mitochondrial creatine kinase isoenzymes differ in stability and membrane binding
-
Schlattner U., and Wallimann T. Octamers of mitochondrial creatine kinase isoenzymes differ in stability and membrane binding. J Biol Chem 275 (2000) 17314-17320
-
(2000)
J Biol Chem
, vol.275
, pp. 17314-17320
-
-
Schlattner, U.1
Wallimann, T.2
-
31
-
-
0842323745
-
Mice lacking the UbCKmit isoform of creatine kinase reveal slower spatial learning acquisition, diminished exploration and habituation, and reduced acoustic startle reflex responses
-
Streijger F., Jost C.R., Oerlemans F., Ellenbroek B.A., Cools A.R., Wieringa B., et al. Mice lacking the UbCKmit isoform of creatine kinase reveal slower spatial learning acquisition, diminished exploration and habituation, and reduced acoustic startle reflex responses. Mol Cell Biochem 1-2 (2004) 305-318
-
(2004)
Mol Cell Biochem
, vol.1-2
, pp. 305-318
-
-
Streijger, F.1
Jost, C.R.2
Oerlemans, F.3
Ellenbroek, B.A.4
Cools, A.R.5
Wieringa, B.6
-
32
-
-
0035879332
-
Inhibition of mitochondrial complex II induces a long-term potentiation of NMDA-mediated synaptic excitation in the striatum requiring endogenous dopamine
-
Calabresi P., Gubellini P., Picconi B., Centonze D., Pisani A., Bonsi P., et al. Inhibition of mitochondrial complex II induces a long-term potentiation of NMDA-mediated synaptic excitation in the striatum requiring endogenous dopamine. J Neurosci 21 (2001) 5110-5120
-
(2001)
J Neurosci
, vol.21
, pp. 5110-5120
-
-
Calabresi, P.1
Gubellini, P.2
Picconi, B.3
Centonze, D.4
Pisani, A.5
Bonsi, P.6
-
33
-
-
0038381516
-
Mitochondrial regulation of synaptic plasticity in the hippocampus
-
Levy M., Faas G.C., Saggau P., Craigen W.J., and Sweatt J.D. Mitochondrial regulation of synaptic plasticity in the hippocampus. J Biol Chem 278 (2003) 17727-17734
-
(2003)
J Biol Chem
, vol.278
, pp. 17727-17734
-
-
Levy, M.1
Faas, G.C.2
Saggau, P.3
Craigen, W.J.4
Sweatt, J.D.5
-
34
-
-
0142074341
-
Oral creatine monohydrate supplementation improves brain performance: a double-blind, placebo-controlled, cross-over trial
-
Rae C., Digney A.L., McEwan S.R., and Bates T.C. Oral creatine monohydrate supplementation improves brain performance: a double-blind, placebo-controlled, cross-over trial. Proc R Soc Lond B Biol Sci 270 (2003) 2147-2150
-
(2003)
Proc R Soc Lond B Biol Sci
, vol.270
, pp. 2147-2150
-
-
Rae, C.1
Digney, A.L.2
McEwan, S.R.3
Bates, T.C.4
-
35
-
-
0016690789
-
The effect of succinic semialdehyde and sodium succinate on the higher nervous activity in normal subjects
-
Saarma J., Saarma M., Aadamsoo A., Jatsa K., Liivamagi J., and Mehilane L. The effect of succinic semialdehyde and sodium succinate on the higher nervous activity in normal subjects. Int Pharmacopsychiatry 10 (1975) 149-156
-
(1975)
Int Pharmacopsychiatry
, vol.10
, pp. 149-156
-
-
Saarma, J.1
Saarma, M.2
Aadamsoo, A.3
Jatsa, K.4
Liivamagi, J.5
Mehilane, L.6
-
36
-
-
0036351166
-
Noninvasive, in vivo approaches to evaluating behavior and exercise physiology in mouse models of mitochondrial disease
-
Graham B.H., David Sweatt J., and Craigen W.J. Noninvasive, in vivo approaches to evaluating behavior and exercise physiology in mouse models of mitochondrial disease. Methods 26 (2002) 364-370
-
(2002)
Methods
, vol.26
, pp. 364-370
-
-
Graham, B.H.1
David Sweatt, J.2
Craigen, W.J.3
-
37
-
-
0026583782
-
The neuropsychological features of mitochondrial myopathies and encephalomyopathies
-
Kartsounis L.D., Troung D.D., Morgan-Hughes J.A., and Harding A.E. The neuropsychological features of mitochondrial myopathies and encephalomyopathies. Arch Neurol 49 (1992) 158-160
-
(1992)
Arch Neurol
, vol.49
, pp. 158-160
-
-
Kartsounis, L.D.1
Troung, D.D.2
Morgan-Hughes, J.A.3
Harding, A.E.4
-
38
-
-
0025761069
-
Effect of postnatal methylmalonate administration on adult rat behavior
-
Dutra J., Wajner M., Wannmacher C.M., Wannmacher L.E., Pires R.F., and Rosa-Junior A. Effect of postnatal methylmalonate administration on adult rat behavior. Braz J Med Biol Res 24 (1991) 595-605
-
(1991)
Braz J Med Biol Res
, vol.24
, pp. 595-605
-
-
Dutra, J.1
Wajner, M.2
Wannmacher, C.M.3
Wannmacher, L.E.4
Pires, R.F.5
Rosa-Junior, A.6
-
39
-
-
0028220040
-
Effects of postnatal methylmalonate administration on neurobehavioral development of rats
-
Mello C.F., Somer J.E., Tavaroni V., Graciolli R., Wu V., Torres G., et al. Effects of postnatal methylmalonate administration on neurobehavioral development of rats. Braz J Med Biol Res 27 (1994) 655-661
-
(1994)
Braz J Med Biol Res
, vol.27
, pp. 655-661
-
-
Mello, C.F.1
Somer, J.E.2
Tavaroni, V.3
Graciolli, R.4
Wu, V.5
Torres, G.6
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