An in vitro model of Fabry disease

Journal of the American Society of Nephrology

Volumn 16, Issue 9, 2005, Pages 2636-2645

  Shu, Liming ^a   Murphy, Hedwig S ^a   Cooling, Laura ^a   Shayman, James A ^a  

^a UNIVERSITY OF MICHIGAN MEDICAL SCHOOL   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ALPHA GALACTOSIDASE; CD31 ANTIGEN; GLOBOTRIAOSYLCERAMIDE; GLYCOLIPID; GLYCOSYLCERAMIDASE; 3',4' ETHYLENEDIOXYPHENYL 2 PALMITOYLAMINO 3 PYRROLIDINO 1 PROPANOL; 3',4'-ETHYLENEDIOXYPHENYL-2-PALMITOYLAMINO-3-PYRROLIDINO-1-PROPANOL; CERAMIDE GLUCOSYLTRANSFERASE; CERAMIDE TRIHEXOSIDE; ENZYME INHIBITOR; GLUCOSYLTRANSFERASE; PROPANOLAMINE DERIVATIVE; PYRROLIDINE DERIVATIVE; RECOMBINANT PROTEIN;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; BIOCHEMISTRY; CARDIOVASCULAR DISEASE; CONTROLLED STUDY; ENDOTHELIUM CELL; FABRY DISEASE; GENETIC ANALYSIS; IN VITRO STUDY; KIDNEY FAILURE; LIPIDOSIS; MOUSE; NEUROPATHY; NONHUMAN; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN SYNTHESIS; VASCULAR DISEASE; WILD TYPE; ANIMAL; C57BL MOUSE; CELL CULTURE; DISEASE MODEL; DRUG ANTAGONISM; DRUG EFFECT; GENETICS; HUMAN; METABOLISM; MOUSE MUTANT; VASCULAR ENDOTHELIUM;

ALPHA-GALACTOSIDASE; ANIMALS; CELLS, CULTURED; DISEASE MODELS, ANIMAL; ENDOTHELIUM, VASCULAR; ENZYME INHIBITORS; FABRY DISEASE; GLUCOSYLTRANSFERASES; HUMANS; MICE; MICE, INBRED C57BL; MICE, KNOCKOUT; PROPANOLAMINES; PYRROLIDINES; RECOMBINANT PROTEINS; TRIHEXOSYLCERAMIDES;

EID: 33644788698     PISSN: 10466673     EISSN: None     Source Type: Journal    
DOI: 10.1681/ASN.2005040383     Document Type: Article

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