Correction of the copper transport defect of Menkes patient fibroblasts by expression of the menkes and Wilson ATPases

Journal of Biological Chemistry

Volumn 273, Issue 47, 1998, Pages 31375-31380

  La Fontaine, Sharon ^a   Firth, Stephen D ^a   Camakaris, James ^b   Englezou, Anna ^c   Theophilos, Michael B ^a   Petris, Michael J ^a,b   Howie, Michelle ^a   Lockhart, Paul J ^a   Greenough, Mark ^b   Brooks, Hilary ^b   Reddel, Roger R ^c   Mercer, Julian F B ^a,d  

^a ROYAL CHILDREN'S HOSPITAL   (Australia)

^b UNIVERSITY OF MELBOURNE   (Australia)

^c CHILDREN'S MEDICAL RESEARCH INSTITUTE   (Australia)

^d DEAKIN UNIVERSITY   (Australia)

Author keywords

[No Author keywords available]

Indexed keywords

ARTICLE; BIOACCUMULATION; COPPER DEFICIENCY; COPPER METABOLISM; HOMEOSTASIS; HUMAN; INTRACELLULAR TRANSPORT; PRIORITY JOURNAL; SYNDROME; WILSON DISEASE;

ADENOSINE TRIPHOSPHATASES; BIOLOGICAL TRANSPORT; CARRIER PROTEINS; CATION TRANSPORT PROTEINS; CELL COMPARTMENTATION; COPPER; FIBROBLASTS; FLUORESCENT ANTIBODY TECHNIQUE; HUMANS; MENKES KINKY HAIR SYNDROME; RECOMBINANT FUSION PROTEINS; RECOMBINANT PROTEINS;

MURINAE;

EID: 0032553535     PISSN: 00219258     EISSN: None     Source Type: Journal    
DOI: 10.1074/jbc.273.47.31375     Document Type: Article

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