Transgenic rescue of neurogenic atrophy in the nmd mouse reveals a role for Ighmbp2 in dilated cardiomyopathy

Human Molecular Genetics

Volumn 13, Issue 11, 2004, Pages 1105-1115

  Maddatu, Terry P ^a   Garvey, Sean M ^b   Schroeder, David G ^a   Hampton, Thomas G ^c   Cox, Gregory A ^a  

^a JACKSON LABORATORY   (United States)

^b DUKE UNIVERSITY   (United States)

^c HARVARD MEDICAL SCHOOL   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

COMPLEMENTARY DNA; HELICASE; IMMUNOGLOBULIN MU BINDING PROTEIN 2; RNA HELICASE; UNCLASSIFIED DRUG;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; AUTOPSY; CELL DENSITY; CELL DIFFERENTIATION; CELL FUNCTION; CELL STRUCTURE; CELL SURVIVAL; CELL TYPE; CONGESTIVE CARDIOMYOPATHY; CONTROLLED STUDY; DEGENERATIVE DISEASE; DNA MODIFICATION; ECHOCARDIOGRAPHY; ELECTROCARDIOGRAM; GENE EXPRESSION; GENE STRUCTURE; GENETIC LINE; HEART FAILURE; HEART MUSCLE CELL; HEREDITARY MOTOR SENSORY NEUROPATHY; HETEROZYGOTE; HISTOPATHOLOGY; IN VIVO STUDY; LUMBAR SPINE; MOTONEURON; MOTOR NEURON DISEASE; MOUSE; MUSCLE CELL; NERVE CELL; NERVE FIBER; NEUROMUSCULAR DISEASE; NONHUMAN; PATHOGENESIS; PRIORITY JOURNAL; PROTEIN FUNCTION; RESPIRATORY FAILURE; SKELETAL MUSCLE; TRANSGENIC MOUSE; VENTRAL ROOT;

ANIMALS; AXONS; CARDIOMYOPATHY, DILATED; CREATINE KINASE; DNA-BINDING PROTEINS; ELECTROCARDIOGRAPHY; FEMALE; GENE EXPRESSION; GENE THERAPY; HEART RATE; MALE; MICE; MICE, NEUROLOGIC MUTANTS; MICE, TRANSGENIC; MUSCLE, SKELETAL; MUSCULAR ATROPHY; MYOCARDIUM; PHOSPHOPYRUVATE HYDRATASE; PROMOTER REGIONS (GENETICS); RATS; SPINAL CORD; SPINAL NERVE ROOTS; TRANSCRIPTION FACTORS;

MUS MUSCULUS;

EID: 2942709863     PISSN: 09646906     EISSN: None     Source Type: Journal    
DOI: 10.1093/hmg/ddh129     Document Type: Article

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