Structural basis of hereditary coproporphyria

Proceedings of the National Academy of Sciences of the United States of America

Volumn 102, Issue 40, 2005, Pages 14232-14237

  Lee, Dong Sun ^a   Flachsová, Eva ^b   Bodnárová, Michaela ^b   Demeler, Borries ^c   Martásek, Pavel ^b   Raman, C S ^a  

^a UNIVERSITY OF TEXAS MEDICAL SCHOOL   (United States)

^b CHARLES UNIVERSITY   (Czech Republic)

^c UNIVERSITY OF TEXAS HEALTH SCIENCE CENTER AT SAN ANTONIO   (United States)

Author keywords

Coproporphyrinogen oxidase; Mitochondria; Oxidative decarboxylation; X ray crystallography

Indexed keywords

ARGININE; ASPARAGINE; ASPARTIC ACID; CITRIC ACID; COPROPORPHYRINOGEN OXIDASE; HEME; HISTIDINE; MONOMER; SERINE;

ALPHA HELIX; ARTICLE; AUTOSOMAL DOMINANT DISORDER; BETA SHEET; CATALYSIS; COPROPORPHYRIA; CRYSTAL STRUCTURE; DECARBOXYLATION; DIMERIZATION; ENZYME ACTIVE SITE; ENZYME ACTIVITY; ENZYME SUBSTRATE COMPLEX; EXON; GENE MUTATION; HEME SYNTHESIS; HEPATIC PORPHYRIA; HUMAN; PRIORITY JOURNAL;

AMINO ACID SEQUENCE; CITRIC ACID; COPROPORPHYRIA, HEREDITARY; COPROPORPHYRINOGEN OXIDASE; CRYSTALLOGRAPHY; DIMERIZATION; HUMANS; MODELS, MOLECULAR; MOLECULAR SEQUENCE DATA; MUTATION; PROTEIN CONFORMATION; SEQUENCE ALIGNMENT; ULTRACENTRIFUGATION;

EID: 26444584539     PISSN: 00278424     EISSN: None     Source Type: Journal    
DOI: 10.1073/pnas.0506557102     Document Type: Article

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