In vitro correction of medium chain acyl CoA dehydrogenase deficiency with a recombinant adenoviral vector

Molecular Genetics and Metabolism

Volumn 85, Issue 2, 2005, Pages 88-95

  Schowalter, David B ^a   Matern, Dietrich ^a   Vockley, Jerry ^b  

^a MAYO CLINIC   (United States)

^b CHILDREN S HOSPITAL OF PITTSBURGH   (United States)

Author keywords

Adenovirus; Co focal microscopy; Human fibroblasts; Medium chain acyl CoA dehydrogenase; Tandem mass spectroscopy

Indexed keywords

ACYLCARNITINE; ADENOVIRUS VECTOR; MEDIUM CHAIN ACYL COENZYME A DEHYDROGENASE; PALMITIC ACID;

ARTICLE; CATALYSIS; CELLULAR DISTRIBUTION; CONFOCAL MICROSCOPY; CONTROLLED STUDY; ELECTRON TRANSPORT; ENZYME DEFICIENCY; FIBROBLAST; HUMAN; HUMAN CELL; IMMUNOHISTOLOGY; IN VITRO STUDY; IN VIVO STUDY; MEDIUM CHAIN ACYL COENZYME A DEHYDROGENASE DEFICIENCY; MITOCHONDRION; MOLECULAR WEIGHT; NONHUMAN; PRIORITY JOURNAL; PROMOTER REGION; PROTEIN EXPRESSION; PROTEIN LOCALIZATION; VIRAL GENE DELIVERY SYSTEM; VIRUS RECOMBINANT; WESTERN BLOTTING;

ACYL-COA DEHYDROGENASE; ADENOVIRIDAE; ANIMALS; CARNITINE; CATTLE; CELL LINE; CYTOMEGALOVIRUS; FIBROBLASTS; GENE TRANSFER TECHNIQUES; GENES, IMMEDIATE-EARLY; GENETIC VECTORS; HUMANS; MASS SPECTROMETRY; PROMOTER REGIONS (GENETICS); RNA 3' POLYADENYLATION SIGNALS;

ADENOVIRIDAE; BOVINAE; CUCUMBER MOSAIC VIRUS; MURINAE;

EID: 19444373026     PISSN: 10967192     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.ymgme.2005.02.006     Document Type: Article

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