Disorders of the mitochondria

Seminars in Liver Disease

Volumn 18, Issue 3, 1998, Pages 237-253

  Treem, William R ^b   Sokol, Ronald J ^a  

^a CHILDREN S HOSPITAL   (United States)

^b NONE

Author keywords

Childhood liver disease; Free radicals; Genetic defects; Oxidative phosphorylation; Respiratory chain

Indexed keywords

ADENOSINE TRIPHOSPHATASE; ALCOHOL; ANTIOXIDANT; CARNITINE; CYTOCHROME C OXIDASE; DICHLOROACETIC ACID; FREE RADICAL; KETONE BODY; LACTIC ACID; MITOCHONDRIAL DNA; PROTON TRANSPORTING ADENOSINE TRIPHOSPHATE SYNTHASE; PYRUVIC ACID; REDUCED NICOTINAMIDE ADENINE DINUCLEOTIDE DEHYDROGENASE (UBIQUINONE); SUCCINATE DEHYDROGENASE (UBIQUINONE); UBIQUINOL CYTOCHROME C REDUCTASE; UBIQUINONE;

ALCOHOL INTOXICATION; CHILDHOOD DISEASE; CLINICAL FEATURE; DISORDERS OF MITOCHONDRIAL FUNCTIONS; ELECTRON TRANSPORT; ENZYME ACTIVITY; FATTY ACID OXIDATION; GENE MUTATION; GENE THERAPY; HUMAN; LIVER DISEASE; LIVER FAILURE; LIVER MITOCHONDRION; LIVER TRANSPLANTATION; NUCLEOTIDE SEQUENCE; OXIDATIVE PHOSPHORYLATION; OXIDATIVE STRESS; PEARSON SYNDROME; PRENATAL DIAGNOSIS; PRIORITY JOURNAL; RESPIRATORY CHAIN; REVIEW; REYE SYNDROME; UREA CYCLE;

EID: 0031713986     PISSN: 02728087     EISSN: None     Source Type: Journal    
DOI: 10.1055/s-2007-1007160     Document Type: Review

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