Molecular effects of homocysteine on cbEGF domain structure: Insights into the pathogenesis of homocystinuria

Journal of Molecular Biology

Volumn 346, Issue 3, 2005, Pages 833-844

  Hutchinson, Sarah ^a   Aplin, Robin T ^b   Webb, Heather ^a   Kettle, Susan ^a   Timmermans, Janneke ^c   Boers, Godfried H J ^c   Handford, Penny A ^a  

^a UNIVERSITY OF OXFORD   (United Kingdom)

^b Henry Wellcome Bldg of Genomic Med ^*  (United Kingdom)

^c RADBOUD UNIVERSITY MEDICAL CENTER   (Netherlands)

Author keywords

Calcium binding; cbEGF domains; Fibrillin 1; Homocysteine; Marfan syndrome

Indexed keywords

DISULFIDE; EPIDERMAL GROWTH FACTOR; HOMOCYSTEINE; NOTCH1 RECEPTOR;

ARTICLE; CALCIUM BINDING; CHEMICAL STRUCTURE; CONNECTIVE TISSUE; DISULFIDE BOND; ELECTROSPRAY MASS SPECTROMETRY; HIGH PERFORMANCE LIQUID CHROMATOGRAPHY; HOMOCYSTINURIA; MOLECULAR INTERACTION; PATHOGENESIS; PATHOGENICITY; PRIORITY JOURNAL; PROTEIN DEGRADATION; PROTEIN DOMAIN; REVERSED PHASE HIGH PERFORMANCE LIQUID CHROMATOGRAPHY;

EID: 13844281063     PISSN: 00222836     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.jmb.2004.11.038     Document Type: Article

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