Defective calcium binding to fibrillin-1: Consequence of an N2144S change for fibrillin-1 structure and function

Journal of Molecular Biology

Volumn 285, Issue 3, 1999, Pages 1277-1287

  Kettle, Susan ^a   Yuan, Xuemei ^b,c   Grundy, Gabrielle ^a   Knott, Vroni ^a   Downing, A Kristina ^b,c   Handford, Penny A ^a,c  

^a UNIVERSITY OF OXFORD   (United Kingdom)

^b UNIVERSITY OF OXFORD   (United Kingdom)

^c UNIVERSITY OF OXFORD   (United Kingdom)

Author keywords

Calcium; cbEGF domain; Fibrillin; Marfan syndrome; TB domain

Indexed keywords

AMINO ACID; EPIDERMAL GROWTH FACTOR; FIBRILLIN; LIGAND; SULFUR 35;

AMINO ACID SUBSTITUTION; AMINO TERMINAL SEQUENCE; ARTICLE; BINDING AFFINITY; BIOSYNTHESIS; CALCIUM BINDING; CONNECTIVE TISSUE; CONNECTIVE TISSUE DISEASE; DISSOCIATION CONSTANT; ESCHERICHIA COLI; EXTRACELLULAR MATRIX; FIBER; FIBROBLAST; GENE MUTATION; MARFAN SYNDROME; NONHUMAN; NUCLEAR MAGNETIC RESONANCE; PRIORITY JOURNAL; PROTEIN FOLDING;

ESCHERICHIA COLI;

EID: 0033593368     PISSN: 00222836     EISSN: None     Source Type: Journal    
DOI: 10.1006/jmbi.1998.2368     Document Type: Article

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