Autoimmune lymphoproliferative syndrome: An inherited disorder with a high incidence of autoimmune cytopenias

Transfusion Medicine and Hemotherapy

Volumn 30, Issue 6, 2003, Pages 270-275

  Stronceka, D ^a   Daleb, J K ^b   Strausb, S E ^b  

^a NATIONAL INSTITUTES OF HEALTH   (United States)

^b NATIONAL INSTITUTE OF ALLERGY AND INFECTIOUS DISEASES   (United States)

Author keywords

Autoimmune hemolytic anemia; Autoimmune lymphoproliferative syndrome; Autoimmune neutropenia; Autoimmune thrombocytopenia; Fas

Indexed keywords

ALPHA INTERFERON; ANTINUCLEAR ANTIBODY; ANTIPARASITIC AGENT; AUTOANTIBODY; AZATHIOPRINE; CASPASE; CD4 ANTIGEN; CD8 ANTIGEN; CYCLOSPORIN A; ERYTHROCYTE ANTIBODY; FAS ANTIGEN; FAS ASSOCIATED DEATH DOMAIN PROTEIN; FAS LIGAND; GRANULOCYTE ANTIBODY; IMMUNOGLOBULIN; INTERLEUKIN 10; INTERLEUKIN 2; METHOTREXATE; MYCOPHENOLIC ACID 2 MORPHOLINOETHYL ESTER; PHOSPHOLIPID ANTIBODY; PREDNISONE; RHEUMATOID FACTOR; RITUXIMAB; T LYMPHOCYTE RECEPTOR ALPHA CHAIN; T LYMPHOCYTE RECEPTOR BETA CHAIN; THROMBOCYTE ANTIBODY; TUMOR NECROSIS FACTOR RECEPTOR; VINCRISTINE;

AGE DISTRIBUTION; ANTIGEN EXPRESSION; APOPTOSIS; AUTOIMMUNE DISEASE; AUTOIMMUNE LYMPHOPROLIFERATIVE SYNDROME; AUTOIMMUNITY; AUTOSOMAL DOMINANT DISORDER; BONE MARROW TRANSPLANTATION; CANCER RISK; CHILDHOOD; CLINICAL FEATURE; CORTICOSTEROID THERAPY; DISEASE ASSOCIATION; DISEASE SEVERITY; GENE MUTATION; GENETIC CODE; HEMOLYTIC ANEMIA; HODGKIN DISEASE; HOMEOSTASIS; HUMAN; IDIOPATHIC THROMBOCYTOPENIC PURPURA; IMMUNOSUPPRESSIVE TREATMENT; INFANCY; LABORATORY TEST; LYMPHADENOPATHY; LYMPHOCYTE FUNCTION; LYMPHOCYTE PROLIFERATION; LYMPHOCYTOSIS; LYMPHOPROLIFERATIVE DISEASE; NEUTROPENIA; NONHODGKIN LYMPHOMA; PROTEIN EXPRESSION; RECEPTOR GENE; REVIEW; SPLENOMEGALY; T LYMPHOCYTE; TREATMENT OUTCOME;

EID: 0347319563     PISSN: 16603796     EISSN: None     Source Type: Journal    
DOI: 10.1159/000075861     Document Type: Review

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