-
1
-
-
0024424270
-
-
Riordan, J. R., Rommens, J. M., Kerem, B., Alon, N., Rozmachel, R., Grzelczak, K., Zielenski, J., Lok, S., Plavsic, N., Chou, J. L., Drumm M. L., Iannuzzi, M. C., Collins, F. S., and Tsui, L.-P. (1989) Science 245, 1066-1073
-
(1989)
Science
, vol.245
, pp. 1066-1073
-
-
Riordan, J.R.1
Rommens, J.M.2
Kerem, B.3
Alon, N.4
Rozmachel, R.5
Grzelczak, K.6
Zielenski, J.7
Lok, S.8
Plavsic, N.9
Chou, J.L.10
Drumm, M.L.11
Iannuzzi, M.C.12
Collins, F.S.13
Tsui, L.-P.14
-
2
-
-
0001752544
-
-
th Ed, McGraw-Hill, New York
-
th Ed., pp. 5121-5188, McGraw-Hill, New York
-
(2001)
Metabolic and Molecular Basis of Inherited Disease
, pp. 5121-5188
-
-
Welsh, M.J.1
Ramsey, B.W.2
Accurso, F.3
Cutting, G.4
-
3
-
-
0034885663
-
-
Tarran, R., Grubb, B. R., Parsons, D., Picher, M., Hirsh, A. J., Davis, C. W., and Boucher, R. C. (2001) Mol. Cell 8, 149-158
-
(2001)
Mol. Cell
, vol.8
, pp. 149-158
-
-
Tarran, R.1
Grubb, B.R.2
Parsons, D.3
Picher, M.4
Hirsh, A.J.5
Davis, C.W.6
Boucher, R.C.7
-
4
-
-
0028914085
-
-
Khan, T. Z., Wagener, J. S., Bost, T., Martinez, J., Accurso, F. J., and Riches, D. W. (1995) Am. J. Respir. Crit. Care Med. 151, 1075-1082
-
(1995)
Am. J. Respir. Crit. Care Med.
, vol.151
, pp. 1075-1082
-
-
Khan, T.Z.1
Wagener, J.S.2
Bost, T.3
Martinez, J.4
Accurso, F.J.5
Riches, D.W.6
-
5
-
-
0032081281
-
-
DiMango, E., Ratner, A. J., Bryan, R., Tabibi, S., and Prince, A. (1998) J. Clin. Invest. 101, 2598-2605
-
(1998)
J. Clin. Invest.
, vol.101
, pp. 2598-2605
-
-
DiMango, E.1
Ratner, A.J.2
Bryan, R.3
Tabibi, S.4
Prince, A.5
-
6
-
-
0032925551
-
-
Elmer, H. L., Brady, K. G., Drumm, M. L., and Kelley, T. J. (1999) Am. J. Physiol. 276, L466-L473
-
(1999)
Am. J. Physiol.
, vol.276
-
-
Elmer, H.L.1
Brady, K.G.2
Drumm, M.L.3
Kelley, T.J.4
-
7
-
-
0028210022
-
-
Engelhardt, J. F., Zepeda, M., Cohn, J. A., Yankaskas, J. R., and Wilson, J. M. (1994) J. Clin. Invest. 93, 737-749
-
(1994)
J. Clin. Invest.
, vol.93
, pp. 737-749
-
-
Engelhardt, J.F.1
Zepeda, M.2
Cohn, J.A.3
Yankaskas, J.R.4
Wilson, J.M.5
-
8
-
-
13344282728
-
-
Rozmahel, R., Wilschanski, M., Matin, A., Plyte, S., Oliver, M., Auerbach, W., Moore, A., Forstner, J., Durie, P., Nadeau, J., Bear, C., and Tsui, L. C. (1996) Nat. Genet. 12, 280-287
-
(1996)
Nat. Genet.
, vol.12
, pp. 280-287
-
-
Rozmahel, R.1
Wilschanski, M.2
Matin, A.3
Plyte, S.4
Oliver, M.5
Auerbach, W.6
Moore, A.7
Forstner, J.8
Durie, P.9
Nadeau, J.10
Bear, C.11
Tsui, L.C.12
-
9
-
-
0026649122
-
-
Snouwaert, J. N., Brigman, K. K., Latour, A. M., Malouf, N. N., Boucher, R. C., Smithies, O., and Koller, B. H. (1992) Science 257, 1083-1088
-
(1992)
Science
, vol.257
, pp. 1083-1088
-
-
Snouwaert, J.N.1
Brigman, K.K.2
Latour, A.M.3
Malouf, N.N.4
Boucher, R.C.5
Smithies, O.6
Koller, B.H.7
-
10
-
-
0028557095
-
-
Zhou, L., Dey, C. R., Wert, S. E., DuVall, M. D., Frizzell, R. A., and Whitsett, J. A. (1994) Science 266, 1705-1708
-
(1994)
Science
, vol.266
, pp. 1705-1708
-
-
Zhou, L.1
Dey, C.R.2
Wert, S.E.3
DuVall, M.D.4
Frizzell, R.A.5
Whitsett, J.A.6
-
11
-
-
0034292343
-
-
Chroneos, Z. C., Wert, S. E., Livingston, J. L., Hassett, D. J., and Whitsett, J. A. (2000) J. Immunol. 165, 3941-3950
-
(2000)
J. Immunol.
, vol.165
, pp. 3941-3950
-
-
Chroneos, Z.C.1
Wert, S.E.2
Livingston, J.L.3
Hassett, D.J.4
Whitsett, J.A.5
-
12
-
-
0035163845
-
-
Cho, R. J., Huang, M., Campbell, M. J., Dong, H., Steinmetz, L., Sapinoso, L., Hampton, G., Elledge, S. J., Davis, R. W., and Lockhart, D. J. (2001) Nat. Genet. 27, 48-54
-
(2001)
Nat. Genet.
, vol.27
, pp. 48-54
-
-
Cho, R.J.1
Huang, M.2
Campbell, M.J.3
Dong, H.4
Steinmetz, L.5
Sapinoso, L.6
Hampton, G.7
Elledge, S.J.8
Davis, R.W.9
Lockhart, D.J.10
-
13
-
-
0035300437
-
-
Notterman, D. A., Alon, U., Sierk, A. J., and Levine, A. J. (2001) Cancer Res. 61, 3124-3130
-
(2001)
Cancer Res.
, vol.61
, pp. 3124-3130
-
-
Notterman, D.A.1
Alon, U.2
Sierk, A.J.3
Levine, A.J.4
-
14
-
-
0037151091
-
-
Whitsett, J. A., Clark, J. C., Picard, L., Tichelaar, J. W., Wert, S. E., Itoh, N., Perl, A-K. T., and Stahlman, M. T. (2002) J. Biol. Chem. 277, 22743-22749
-
(2002)
J. Biol. Chem.
, vol.277
, pp. 22743-22749
-
-
Whitsett, J.A.1
Clark, J.C.2
Picard, L.3
Tichelaar, J.W.4
Wert, S.E.5
Itoh, N.6
Perl, A-K.T.7
Stahlman, M.T.8
-
15
-
-
0035805534
-
-
Cafferata, E. G. A., Guerrico, A. M. G., Pivetta, O. H., and Santa-Coloma, T. A. (2001) J. Biol. Chem. 276, 15441-15444
-
(2001)
J. Biol. Chem.
, vol.276
, pp. 15441-15444
-
-
Cafferata, E.G.A.1
Guerrico, A.M.G.2
Pivetta, O.H.3
Santa-Coloma, T.A.4
-
16
-
-
0028866431
-
-
Pittman, N., Shue, G., LeLeiko, N. S., and Walsh, M. J. (1995) J. Biol. Chem. 270, 28848-28857
-
(1995)
J. Biol. Chem.
, vol.270
, pp. 28848-28857
-
-
Pittman, N.1
Shue, G.2
LeLeiko, N.S.3
Walsh, M.J.4
-
18
-
-
0027312715
-
-
Shen, B. Q., Barthelson, R. A., Skach, W., Gruenert, D. C., Sigal, E., Mrsny R. J., and Widdicombe, J. H. (1993) J. Biol. Chem. 268, 19070-19075
-
(1993)
J. Biol. Chem.
, vol.268
, pp. 19070-19075
-
-
Shen, B.Q.1
Barthelson, R.A.2
Skach, W.3
Gruenert, D.C.4
Sigal, E.5
Mrsny, R.J.6
Widdicombe, J.H.7
-
19
-
-
0033612571
-
-
Heyninck, K., De Valck, D., Vanden Berghe, W., Van Criekinge, W., Contreras, R., Fiers, W., Haegeman, G., and Beyaert, R. (1999) J. Cell Biol. 145, 1471-1482
-
(1999)
J. Cell Biol.
, vol.145
, pp. 1471-1482
-
-
Heyninck, K.1
De Valck, D.2
Vanden Berghe, W.3
Van Criekinge, W.4
Contreras, R.5
Fiers, W.6
Haegeman, G.7
Beyaert, R.8
-
22
-
-
17344381330
-
-
Thomas, G. R., Costelloe, E. A., Lunn, D. P., Stacey, K. J., Delaney, S. J., Passey, R., McGlinn, E. C., McMorran, B. J., Ahadizadeh, A., Geczy, C. L., Wainwright, B. J., and Hume, D. A. (2000) J. Immunol. 164, 3870-3877
-
(2000)
J. Immunol.
, vol.164
, pp. 3870-3877
-
-
Thomas, G.R.1
Costelloe, E.A.2
Lunn, D.P.3
Stacey, K.J.4
Delaney, S.J.5
Passey, R.6
McGlinn, E.C.7
McMorran, B.J.8
Ahadizadeh, A.9
Geczy, C.L.10
Wainwright, B.J.11
Hume, D.A.12
-
23
-
-
0035794188
-
-
Boot, R. G., Blommaart, E. F. C., Swart, E., Ghauharali-van der Vlugt, K., Bijl, N., Moe, C., Place, A., and Aerts, J. M. F. G. (2001) J. Biol. Chem. 276, 6770-6778
-
(2001)
J. Biol. Chem.
, vol.276
, pp. 6770-6778
-
-
Boot, R.G.1
Blommaart, E.F.C.2
Swart, E.3
Ghauharali-van der Vlugt, K.4
Bijl, N.5
Moe, C.6
Place, A.7
Aerts, J.M.F.G.8
-
24
-
-
16044371529
-
-
Rankin, J. A., Picarella, D. E., Temann, U.-A., Prasad, B., Geba, G., DiCosmo, B., Stripp, B., Whitsett, J., Tarallo, A., and Flavell, R. A. (1996) Proc. Natl. Acad. Sci. U. S. A. 93, 7821-7825
-
(1996)
Proc. Natl. Acad. Sci. U. S. A.
, vol.93
, pp. 7821-7825
-
-
Rankin, J.A.1
Picarella, D.E.2
Temann, U.-A.3
Prasad, B.4
Geba, G.5
DiCosmo, B.6
Stripp, B.7
Whitsett, J.8
Tarallo, A.9
Flavell, R.A.10
-
25
-
-
0025270168
-
-
Fukunaga, R., Ishizaka-Ikeda, E., Seto, Y., and Nagataet, S. (1990) Cell 61, 341-350
-
(1990)
Cell
, vol.61
, pp. 341-350
-
-
Fukunaga, R.1
Ishizaka-Ikeda, E.2
Seto, Y.3
Nagataet, S.4
-
26
-
-
0031906851
-
-
Relaix, F., Wei, X-J., Wu, X., and Sassoon, D. A. (1998) Nat. Genet. 18, 287-291
-
(1998)
Nat. Genet.
, vol.18
, pp. 287-291
-
-
Relaix, F.1
Wei, X.-J.2
Wu, X.3
Sassoon, D.A.4
-
27
-
-
0037076416
-
-
Schroeder, T. H., Lee, M. M., Yacono, P. W., Cannon, C. L., Gerceker, A. A., Golan, D. E., and Pier, G. B. (2002) Proc. Natl. Acad. Sci. U. S. A. 99, 6907-6912
-
(2002)
Proc. Natl. Acad. Sci. U. S. A.
, vol.99
, pp. 6907-6912
-
-
Schroeder, T.H.1
Lee, M.M.2
Yacono, P.W.3
Cannon, C.L.4
Gerceker, A.A.5
Golan, D.E.6
Pier, G.B.7
-
28
-
-
0035008989
-
-
Chanson, M., Berclaz, P.-Y., Scerri, I., Dudez, T., Wernke-Dollries, K., Pizurki, L., Pavirani, A., Fiedler, M. A., and Suter, S. (2001) Am. J. Pathol. 158, 1775-1784
-
(2001)
Am. J. Pathol.
, vol.158
, pp. 1775-1784
-
-
Chanson, M.1
Berclaz, P.-Y.2
Scerri, I.3
Dudez, T.4
Wernke-Dollries, K.5
Pizurki, L.6
Pavirani, A.7
Fiedler, M.A.8
Suter, S.9
-
30
-
-
0037023764
-
-
Gelman, M. S., Kannegaard, E. S., and Kopito, R. R. (2002) J. Biol. Chem. 277, 11709-11714
-
(2002)
J. Biol. Chem.
, vol.277
, pp. 11709-11714
-
-
Gelman, M.S.1
Kannegaard, E.S.2
Kopito, R.R.3
-
31
-
-
0037053375
-
-
Hu, X., Bryington, M., Fisher, A. B., Liang, X., Zhang, S., Cui, D., Datta, I., and Zuckerman, K. S. (2002) J. Biol. Chem. 277, 16528-16537
-
(2002)
J. Biol. Chem.
, vol.277
, pp. 16528-16537
-
-
Hu, X.1
Bryington, M.2
Fisher, A.B.3
Liang, X.4
Zhang, S.5
Cui, D.6
Datta, I.7
Zuckerman, K.S.8
-
32
-
-
0031085545
-
-
Tanahashi, N., Yokota, K., Ahn, J. Y., Chung, C. H., Fujiwara, T., Takahashi, E., DeMartino, G. N., Slaughter, C. A., Toyonaga, T., Yamamura, K., Shimbara, N., and Tanaka, K. (1997) Genes Cells 2, 195-211
-
(1997)
Genes Cells
, vol.2
, pp. 195-211
-
-
Tanahashi, N.1
Yokota, K.2
Ahn, J.Y.3
Chung, C.H.4
Fujiwara, T.5
Takahashi, E.6
DeMartino, G.N.7
Slaughter, C.A.8
Toyonaga, T.9
Yamamura, K.10
Shimbara, N.11
Tanaka, K.12
-
36
-
-
0029861046
-
-
Biwersi, J., Emans, N., and Verkman, A. S. (1996) Proc. Natl. Acad. Sci. U. S. A. 93, 12484-12489
-
(1996)
Proc. Natl. Acad. Sci. U. S. A.
, vol.93
, pp. 12484-12489
-
-
Biwersi, J.1
Emans, N.2
Verkman, A.S.3
-
37
-
-
0037134419
-
-
Poschet, J. F., Skidmore, J., Boucher, J. C., Firoved, A. M., Van Dyke, R. W., and Deretic, V. (2002) J. Biol. Chem. 277, 13959-13965
-
(2002)
J. Biol. Chem.
, vol.277
, pp. 13959-13965
-
-
Poschet, J.F.1
Skidmore, J.2
Boucher, J.C.3
Firoved, A.M.4
Van Dyke, R.W.5
Deretic, V.6
-
38
-
-
0034235848
-
-
Thiery, E., Gosset, P., Damotte, D., Delezoide, A. L., de Saint-Sauveur, N., Vayssettes, C., and Creau, N. (2000) Mech. Dev. 95, 313-316
-
(2000)
Mech. Dev.
, vol.95
, pp. 313-316
-
-
Thiery, E.1
Gosset, P.2
Damotte, D.3
Delezoide, A.L.4
De Saint-Sauveur, N.5
Vayssettes, C.6
Creau, N.7
-
40
-
-
0031861717
-
-
Kurschner, C., Mermelstein, P. G., Holden, W. T., and Surmeier, D. J. (1998) Mol. Cell Neurosci. 11, 161-172
-
(1998)
Mol. Cell Neurosci.
, vol.11
, pp. 161-172
-
-
Kurschner, C.1
Mermelstein, P.G.2
Holden, W.T.3
Surmeier, D.J.4
-
41
-
-
0027305539
-
-
Wilkins, M. R., Nunez, D. J., and Wharton, J. (1993) J. Endocrinol. 137, 347-359
-
(1993)
J. Endocrinol.
, vol.137
, pp. 347-359
-
-
Wilkins, M.R.1
Nunez, D.J.2
Wharton, J.3
-
42
-
-
0027772318
-
-
Geary, C. A., Goy, M. F., and Boucher, R. C. (1993) Am. J. Physiol. 265, L598-L605
-
(1993)
Am. J. Physiol.
, vol.265
-
-
Geary, C.A.1
Goy, M.F.2
Boucher, R.C.3
-
43
-
-
0032728779
-
-
Chatterjee, P. K., Hawksworth, G. M., and McLay, J. S. (1999) Exp. Nephrol. 7, 438-448
-
(1999)
Exp. Nephrol.
, vol.7
, pp. 438-448
-
-
Chatterjee, P.K.1
Hawksworth, G.M.2
McLay, J.S.3
-
44
-
-
0030900255
-
-
Kelley, T. J., Thomas, K., Milgram, L. J., and Drumm, M. L. (1997) Proc. Natl. Acad. Sci. U. S. A. 94, 2604-2608
-
(1997)
Proc. Natl. Acad. Sci. U. S. A.
, vol.94
, pp. 2604-2608
-
-
Kelley, T.J.1
Thomas, K.2
Milgram, L.J.3
Drumm, M.L.4
-
46
-
-
0033525230
-
-
Leblais, V., Demolombe, S., Vallette, G., Langin, D., Baró, I., Escande, D., and Gauthier, C. (1999) J. Biol. Chem. 274, 6107-6113
-
(1999)
J. Biol. Chem.
, vol.274
, pp. 6107-6113
-
-
Leblais, V.1
Demolombe, S.2
Vallette, G.3
Langin, D.4
Baró, I.5
Escande, D.6
Gauthier, C.7
-
47
-
-
0035906714
-
-
Karthikeyan, S., Leung, T., Birrane, G., Webster, G., and Ladias, J. A. (2001) J. Mol. Biol. 308, 963-973
-
(2001)
J. Mol. Biol.
, vol.308
, pp. 963-973
-
-
Karthikeyan, S.1
Leung, T.2
Birrane, G.3
Webster, G.4
Ladias, J.A.5
|