Ethylmalonic acid inhibits mitochondrial creatine kinase activity from cerebral cortex of young rats in vitro

Neurochemical Research

Volumn 28, Issue 5, 2003, Pages 771-777

  Leipnitz, Guilhian ^a   Schuck, Patrícia F ^a   Ribeiro, César A J ^a   Dalcin, Karina B ^a   Assis, Dênis R ^a   Barschak, Alethea G ^a   Pulrolnik, Vânia ^a   Wannmacher, Clóvis M D ^a   Wyse, Angela T S ^a   Wajner, Moacir ^a,b,c  

^a FEDERAL UNIVERSITY OF RIO GRANDE DO SUL   (Brazil)

^b HOSPITAL DE CLÍNICAS DE PORTO ALEGRE   (Brazil)

^c UNIVERSIDADE LUTERANA DO BRASIL   (Brazil)

Author keywords

Antioxidants; Cytosolic creatine kinase; Ethylmalonic acid; Ethylmalonic aciduria; Mitochondrial creatine kinase; Short chain acyl CoA dehydrogenase deficiency

Indexed keywords

ACYL COENZYME A DEHYDROGENASE; ALPHA TOCOPHEROL; ANTIOXIDANT; ASCORBIC ACID; ETHYLMALONIC ACID; GLUTATHIONE; ISOENZYME; MALONIC ACID DERIVATIVE; N(G) NITROARGININE METHYL ESTER; NITRIC OXIDE SYNTHASE INHIBITOR; UNCLASSIFIED DRUG;

ANIMAL TISSUE; ARTICLE; BRAIN CORTEX; CONCENTRATION RESPONSE; CONTROLLED STUDY; CULTURE MEDIUM; CYTOSOL; ENZYME ACTIVITY; ENZYME DEFICIENCY; ENZYME INHIBITION; HEART MUSCLE; HOMEOSTASIS; MITOCHONDRION; NONHUMAN; PRIORITY JOURNAL; RAT; RAT STRAIN; SKELETAL MUSCLE; SYMPTOM; TISSUE HOMOGENATE;

ANIMALS; CEREBRAL CORTEX; CREATINE KINASE; CYTOSOL; MALONATES; MITOCHONDRIA; MITOCHONDRIA, HEART; MITOCHONDRIA, MUSCLE; MUSCLE, SKELETAL; ORGAN SPECIFICITY; RATS; RATS, WISTAR;

ANIMALIA; PRIACANTHUS HAMRUR; RATTUS NORVEGICUS;

EID: 0037403740     PISSN: 03643190     EISSN: None     Source Type: Journal    
DOI: 10.1023/A:1022874103630     Document Type: Article

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