Preserved myelin integrity and reduced axonopathy in connexin32-deficient mice lacking the recombination activating gene-1

Brain

Volumn 126, Issue 4, 2003, Pages 804-813

  Kobsar, I ^a   Berghoff, M ^a   Samsam, M ^a   Wessig, C ^a   Maurer M ^a   Toyka, K V ^a   Martini, Rudolf ^a  

^a UNIVERSITY OF WÜRZBURG   (Germany)

Author keywords

Charcot Marie Tooth neuropathy; Connexin32; Endoneurial macrophages; Peripheral nervous system; T lymphocytes

Indexed keywords

CONNEXIN 32; MYELIN; RAG1 PROTEIN; GAP JUNCTION PROTEIN; GJA6 PROTEIN, RAT;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; B LYMPHOCYTE; DEGENERATION; DEMYELINATING NEUROPATHY; DOMINANT INHERITANCE; ENDONEURIUM; FEMALE; HEREDITARY MOTOR SENSORY NEUROPATHY; HETEROZYGOSITY; IMMUNOCOMPETENT CELL; IMMUNOPATHOGENESIS; KNOCKOUT MOUSE; MACROPHAGE; MALE; MOUSE; NONHUMAN; PERIPHERAL NERVOUS SYSTEM; PRIORITY JOURNAL; SCHWANN CELL; T LYMPHOCYTE; X CHROMOSOME LINKAGE; ANIMAL; C57BL MOUSE; DEMYELINATING DISEASE; ELECTRON MICROSCOPY; GENE; GENETICS; GENOTYPE; HETEROZYGOTE; IMMUNOLOGY; INNERVATION; LYMPHOCYTE COUNT; LYMPHOCYTOPENIA; MYELIN SHEATH; NERVE FIBER; PATHOLOGY; SKELETAL MUSCLE; UPREGULATION;

ANIMALS; AXONS; B-LYMPHOCYTES; CHARCOT-MARIE-TOOTH DISEASE; CONNEXINS; DEMYELINATING DISEASES; GENES, RAG-1; GENOTYPE; HETEROZYGOTE; LYMPHOCYTE COUNT; LYMPHOPENIA; MACROPHAGES; MICE; MICE, INBRED C57BL; MICROSCOPY, ELECTRON; MUSCLE, SKELETAL; MYELIN SHEATH; T-LYMPHOCYTES; UP-REGULATION;

EID: 0037378129     PISSN: 00068950     EISSN: None     Source Type: Journal    
DOI: 10.1093/brain/awg072     Document Type: Article

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