Molecular mechanism of copper transport in Wilson disease

Environmental Health Perspectives

Volumn 110, Issue SUPPL. 5, 2002, Pages 695-698

  Fatemi, Negah ^a   Sarkar, Bibudhendra ^a  

^a HOSPITAL FOR SICK CHILDREN RESEARCH INSTITUTE   (Canada)

Author keywords

ATP7B ZntA chimera; Copper binding; Copper trafficking; Copper transport; Copper ATPase; Nucleotide binding domain; P type ATPases; Phosphorylation domain; Wilson disease; Wilson disease gene

Indexed keywords

ADENOSINE TRIPHOSPHATASE; ADENOSINE TRIPHOSPHATE; BINDING PROTEIN; CARRIER PROTEIN; COPPER; CYSTEINE; HEAVY METAL; NUCLEOTIDE BINDING PROTEIN; ZINC;

AMINO TERMINAL SEQUENCE; ARTICLE; AUTOSOMAL RECESSIVE DISORDER; BINDING AFFINITY; BINDING COMPETITION; CIRCULAR DICHROISM; COPPER METABOLISM; CYTOSOL; ENZYME ACTIVITY; HUMAN; LIVER DISEASE; METAL BINDING; MOLECULAR MECHANICS; NEUROLOGIC DISEASE; OXIDATION; PRIORITY JOURNAL; PROTEIN ANALYSIS; PROTEIN BINDING; PROTEIN CONFORMATION; PROTEIN DOMAIN; PROTEIN EXPRESSION; PROTEIN FUNCTION; PROTEIN MOTIF; PROTEIN PHOSPHORYLATION; PROTEIN PURIFICATION; SYMPTOM; TRANSPORT KINETICS; WILSON DISEASE;

EID: 0036801448     PISSN: 00916765     EISSN: None     Source Type: Journal    
DOI: 10.1289/ehp.02110s5695     Document Type: Article

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