Lysosomal multienzyme complex: Biochemistry, genetics, and molecular pathophysiology

Progress in Nucleic Acid Research and Molecular Biology

Volumn 69, Issue , 2001, Pages 81-94

  Pshezhetsky, Alexey V ^a   Ashmarina, Mila ^a  

^a UNIVERSITY OF MONTREAL   (Canada)

Author keywords

[No Author keywords available]

Indexed keywords

BETA GALACTOSIDASE; CARBOXYPEPTIDASE; CARBOXYPEPTIDASE A; CELL SURFACE RECEPTOR; ELASTIN BINDING PROTEINS; ELASTIN-BINDING PROTEINS; GALNS PROTEIN, HUMAN; MULTIENZYME COMPLEX; N ACETYLGALACTOSAMINE 4 SULFATASE; SIALIDASE;

CELL MEMBRANE; CHEMICAL STRUCTURE; CHEMISTRY; ENZYMOLOGY; GENETICS; GM1 GANGLIOSIDOSIS; HUMAN; LYSOSOME; LYSOSOME STORAGE DISEASE; MORQUIO SYNDROME; MUCOLIPIDOSIS; PHYSIOLOGY; PROTEIN CONFORMATION; REVIEW;

BETA-GALACTOSIDASE; CARBOXYPEPTIDASES; CARBOXYPEPTIDASES A; CELL MEMBRANE; CHONDROITINSULFATASES; GANGLIOSIDOSIS, GM1; HUMANS; LYSOSOMAL STORAGE DISEASES; LYSOSOMES; MODELS, MOLECULAR; MUCOLIPIDOSES; MUCOPOLYSACCHARIDOSIS IV; MULTIENZYME COMPLEXES; NEURAMINIDASE; PROTEIN CONFORMATION; RECEPTORS, CELL SURFACE;

EID: 0035224941     PISSN: 00796603     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0079-6603(01)69045-7     Document Type: Review

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