Neuronal trafficking of palmitoyl protein thioesterase provides an excellent model to study the effects of different mutations which cause infantile neuronal ceroid lipofuscinocis

Molecular and Cellular Neuroscience

Volumn 18, Issue 2, 2001, Pages 131-140

  Salonen, Tarja ^a   Heinonen Kopra, Outi ^a   Vesa, Jouni ^b   Jalanko, Anu ^a  

^a NATIONAL PUBLIC HEALTH INSTITUTE   (Finland)

^b UNIVERSITY OF CALIFORNIA   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

PALMITOYL PROTEIN THIOESTERASE;

ANIMAL CELL; ARTICLE; CELL CULTURE; CELLULAR DISTRIBUTION; DISEASE SEVERITY; ENDOPLASMIC RETICULUM; ENZYME ACTIVITY; GENE MUTATION; GENETIC TRANSFECTION; GENOTYPE; HUMAN; HUMAN CELL; MODEL; NERVE CELL; NEURONAL CEROID LIPOFUSCINOSIS; NONHUMAN; ONSET AGE; PHENOTYPE; PRIORITY JOURNAL; PROTEIN LOCALIZATION;

ANIMALIA;

EID: 0034848598     PISSN: 10447431     EISSN: None     Source Type: Journal    
DOI: 10.1006/mcne.2001.1010     Document Type: Article

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