Batten's disease: Clues to neuronal protein catabolism in lysosomes

Journal of Neuroscience Research

Volumn 60, Issue 2, 2000, Pages 133-140

  Dawson, Glyn ^a   Cho, Seongeun ^a  

^a UNIVERSITY OF CHICAGO   (United States)

Author keywords

Batten disease; Lysosomal storage disease; Neuronal ceroid lipofuscinosis; Proteases; Protein palmitoylation

Indexed keywords

CATHEPSIN D; DOLICHOL PHOSPHATE MANNOSE; GENE PRODUCT; GLYCOPROTEIN; MEMBRANE PROTEIN; NERVE PROTEIN; PALMITOYL PROTEIN THIOESTERASE; PEPTIDASE;

BRAIN CELL; DISEASE CLASSIFICATION; GENE MUTATION; HUMAN; LYSOSOME; LYSOSOME STORAGE DISEASE; NERVE CELL NECROSIS; NERVE DEGENERATION; NEURONAL CEROID LIPOFUSCINOSIS; ONSET AGE; PALMITOYLATION; PRIORITY JOURNAL; PROTEIN DEGRADATION; PROTEIN MODIFICATION; SHORT SURVEY;

ANIMALS; BRAIN; HUMANS; LYSOSOMES; NERVE TISSUE PROTEINS; NEURONAL CEROID-LIPOFUSCINOSES;

EID: 0034656090     PISSN: 03604012     EISSN: None     Source Type: Journal    
DOI: 10.1002/(SICI)1097-4547(20000415)60:2<133::AID-JNR1>3.0.CO;2-3     Document Type: Short Survey

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