Vascular endothelial dysfunction resulting from L-arginine deficiency in a patient with lysinuric protein intolerance

Journal of Clinical Investigation

Volumn 108, Issue 5, 2001, Pages 717-724

  Kamada, Yoshihiro ^a   Nagaretani, Hiroyuki ^a   Tamura, Shinji ^a,b   Ohama, Tohru ^a   Maruyama, Takao ^a   Hiraoka, Hisatoyo ^a   Yamashita, Shizuya ^a   Yamada, Akira ^a   Kiso, Shinichi ^a   Inui, Yoshiaki ^a   Ito, Nobuyuki ^a   Kayanoki, Yoshiro ^a   Kawata, Sumio ^a   Matsuzawa, Yuji ^a  

^a OSAKA UNIVERSITY   (Japan)

^b OSAKA UNIVERSITY GRADUATE SCHOOL OF MEDICINE   (Japan)

Author keywords

[No Author keywords available]

Indexed keywords

AMINO ACID; AMMONIA; ARGININE; CARBON 13; DNA; GLYCERYL TRINITRATE; LYSINE; NITRATE; NITRIC OXIDE; NITRITE; RNA;

ADULT; AMINO ACID DEFICIENCY; AMINO ACID TRANSPORT; ARTERY DIAMETER; ARTICLE; AUTOSOMAL RECESSIVE DISORDER; BRACHIAL ARTERY; CASE REPORT; CONTROLLED STUDY; ECHOGRAPHY; EXERCISE TEST; GENE MUTATION; GENETIC DISORDER; GENOME; HUMAN; HUMAN CELL; ISCHEMIC HEART DISEASE; MALE; NUCLEOTIDE SEQUENCE; POSITRON EMISSION TOMOGRAPHY; PRIORITY JOURNAL; REVERSE TRANSCRIPTION POLYMERASE CHAIN REACTION; TREADMILL EXERCISE; VASCULAR ENDOTHELIUM; VASCULAR SMOOTH MUSCLE; VASODILATATION;

ADULT; AMINO ACID METABOLISM, INBORN ERRORS; AMINO ACID TRANSPORT SYSTEMS, BASIC; ARGININE; CARRIER PROTEINS; CORONARY ANGIOGRAPHY; ENDOTHELIUM, VASCULAR; EXERCISE TEST; HEART; HEMODYNAMIC PROCESSES; HUMANS; MALE; MEMBRANE PROTEINS; MUTATION; NITRIC OXIDE; TOMOGRAPHY, EMISSION-COMPUTED; VASODILATION;

EID: 0034800081     PISSN: 00219738     EISSN: None     Source Type: Journal    
DOI: 10.1172/JCI200111260     Document Type: Article

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