The diabetes-associated 3243 mutation in the mitochondrial tRNA(Leu(UUR)) gene causes severe mitochondrial dysfunction without a strong decrease in protein synthesis rate

Journal of Biological Chemistry

Volumn 274, Issue 42, 1999, Pages 29744-29748

  Janssen, George M C ^a   Maassen, J Antonie ^a   Van Den Ouweland, Johannes M W ^a,b  

^a LEIDEN UNIVERSITY MEDICAL CENTER   (Netherlands)

^b ISALA HOSPITAL   (Netherlands)

Author keywords

[No Author keywords available]

Indexed keywords

MITOCHONDRIAL RNA;

ARTICLE; DIABETES MELLITUS; DISORDERS OF MITOCHONDRIAL FUNCTIONS; DNA SEQUENCE; GENE MUTATION; HUMAN; HUMAN CELL; MITOCHONDRIAL RESPIRATION; NUCLEIC ACID BASE SUBSTITUTION; PRIORITY JOURNAL; PROTEIN DEGRADATION; PROTEIN SYNTHESIS;

CELLS, CULTURED; DIABETES MELLITUS; DNA, MITOCHONDRIAL; HUMANS; MITOCHONDRIA; MUTATION; OXYGEN; PROTEIN BIOSYNTHESIS; RNA, TRANSFER, LEU;

EID: 0033569992     PISSN: 00219258     EISSN: None     Source Type: Journal    
DOI: 10.1074/jbc.274.42.29744     Document Type: Article

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