Heritable disorder resembling neuronal storage disease in mice expressing prion protein with deletion of an α-helix

Nature Medicine

Volumn 3, Issue 7, 1997, Pages 750-755

  Muramoto, Tamaki ^a   DeArmond, Stephen J ^a   Scott, Michael ^a   Telling, Glenn C ^a   Cohen, Fred E ^a   Prusiner, Stanley B ^a  

^a UNIVERSITY OF CALIFORNIA   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ANIMAL EXPERIMENT; ANIMAL TISSUE; ARTICLE; BRAIN DISEASE; ENDOPLASMIC RETICULUM; GENE DELETION; LIPIDOSIS; MOUSE; NONHUMAN; PRION; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN SECONDARY STRUCTURE;

ANIMALS; GENETIC DISEASES, INBORN; HUMANS; INCLUSION BODIES; MICE; MICE, INBRED C57BL; MICE, TRANSGENIC; MUTATION; PRION DISEASES; PRIONS; PROTEIN STRUCTURE, SECONDARY; SEQUENCE DELETION; STRUCTURE-ACTIVITY RELATIONSHIP;

ANIMALIA; MUS MUSCULUS;

EID: 0030811015     PISSN: 10788956     EISSN: None     Source Type: Journal    
DOI: 10.1038/nm0797-750     Document Type: Article

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