Hepatic α-oxidation of phytanic acid: A revised pathway

Advances in Experimental Medicine and Biology

Volumn 466, Issue , 2000, Pages 273-281

  Van Veldhoven, P P ^a   Mannaerts, G P ^a   Casteels, M ^a   Croes, K ^a  

^a UNIVERSITY OF LEUVEN   (Belgium)

Author keywords

[No Author keywords available]

Indexed keywords

2 OXOGLUTARIC ACID; ACYL COENZYME A; ADENOSINE TRIPHOSPHATE; ALDEHYDE; ALDEHYDE DEHYDROGENASE; ASCORBIC ACID; CARBON DIOXIDE; COENZYME A; FATTY ACID; FORMIC ACID; FORMIC ACID DERIVATIVE; GLUTATHIONE; IRON; LONG CHAIN FATTY ACID COENZYME A LIGASE; MAGNESIUM; NICOTINAMIDE ADENINE DINUCLEOTIDE; OXYGEN; OXYGENASE; PHYTANIC ACID;

ANIMAL TISSUE; CONFERENCE PAPER; FATTY ACID METABOLISM; FATTY ACID OXIDATION; HUMAN; HUMAN TISSUE; HYDROLYSIS; HYDROXYLATION; LIVER CELL; LIVER CYTOSOL; LIVER HOMOGENATE; LIVER METABOLISM; NONHUMAN; PRIORITY JOURNAL; RAT;

ANIMALS; COENZYME A; HUMANS; LIVER; MODELS, CHEMICAL; OXIDATION-REDUCTION; PHYTANIC ACID; RATS;

ANIMALIA;

EID: 0034468869     PISSN: 00652598     EISSN: None     Source Type: Book Series    
DOI: None     Document Type: Conference Paper

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52. Refsum disease is caused by mutations in the phytanoyl-CoA hydroxylase gene