Phytanic acid oxidation: Normal activation and transport yet defective α-hydroxylation of phytanic acid in peroxisomes from Refsum disease and rhizomelic chondrodysplasia punctata

Journal of Lipid Research

Volumn 37, Issue 5, 1996, Pages 1137-1143

  Pahan, Kalipada ^a   Khan, Mushfiquddin ^a   Singh, Inderjit ^a  

^a MEDICAL UNIVERSITY OF SOUTH CAROLINA   (United States)

Author keywords

oxidation; Refsum disease

Indexed keywords

ACYL COENZYME A; ADENOSINE TRIPHOSPHATE; MAGNESIUM CHLORIDE; OXYGENASE; PHYTANIC ACID;

ARTICLE; CELLULAR DISTRIBUTION; CHONDRODYSPLASIA PUNCTATA; CONTROLLED STUDY; DECARBOXYLATION; FATTY ACID METABOLISM; FATTY ACID OXIDATION; FATTY ACID TRANSPORT; HUMAN; HUMAN CELL; HYDROXYLATION; PEROXISOME; PRIORITY JOURNAL; REFSUM DISEASE; SKIN FIBROBLAST;

BIOLOGICAL TRANSPORT; CELLS, CULTURED; CHONDRODYSPLASIA PUNCTATA, RHIZOMELIC; COENZYME A; FIBROBLASTS; HUMANS; HYDROXYLATION; MICROBODIES; OXIDATION-REDUCTION; PHYTANIC ACID; REFERENCE VALUES; REFSUM DISEASE;

EID: 0029898759     PISSN: 00222275     EISSN: None     Source Type: Journal    
DOI: None     Document Type: Article

References (25)

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