Spinocerebellar ataxia type 1 - Modeling the pathogenesis of a polyglutamine neurodegenerative disorder in transgenic mice

Journal of Neuropathology and Experimental Neurology

Volumn 59, Issue 4, 2000, Pages 265-270

  Clark, H Brent ^a   Orr, Harry T ^a  

^a UNIVERSITY OF MINNESOTA MEDICAL SCHOOL   (United States)

Author keywords

Ataxin 1; CAG repeat; Purkinje cell

Indexed keywords

POLYGLUTAMINE;

AMINO ACID SUBSTITUTION; ANIMAL EXPERIMENT; ANIMAL MODEL; AUTOSOMAL DOMINANT INHERITANCE; CEREBELLAR ATAXIA; CHROMOSOME 6; CONTROLLED STUDY; HLA SYSTEM; MOUSE; NERVE DEGENERATION; NEUROPATHOLOGY; NONHUMAN; PATHOGENESIS; PRIORITY JOURNAL; PURKINJE CELL; REVIEW; TRANSGENIC MOUSE; TRINUCLEOTIDE REPEAT;

EID: 0034072172     PISSN: 00223069     EISSN: None     Source Type: Journal    
DOI: 10.1093/jnen/59.4.265     Document Type: Review

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