Bile acid synthetic defects and liver disease

Pediatric and Developmental Pathology

Volumn 3, Issue 1, 2000, Pages 1-16

  Bove, Kevin E ^a,c   Daugherty, Cynthia C ^a   Tyson, Wes ^b   Mierau, Gary ^b   Heubi, James E ^a   Balistreri, William F ^a   Setchell, Kenneth D R ^a  

^a UNIVERSITY OF CINCINNATI COLLEGE OF MEDICINE   (United States)

^b CHILDREN S HOSPITAL   (United States)

^c CINCINNATI CHILDREN'S HOSPITAL MEDICAL CENTER   (United States)

Author keywords

Bile acid synthesis; Fat soluble vitamin deficiency; Liver disease; Metabolic defects; Neonatal hepatitis

Indexed keywords

BILE ACID SYNTHESIS; CLINICAL FEATURE; HUMAN; INBORN ERROR OF METABOLISM; LIVER DISEASE; NEWBORN HEPATITIS; PATHOGENESIS; PRIORITY JOURNAL; REVIEW;

3-HYDROXYSTEROID DEHYDROGENASES; ANIMALS; BILE ACIDS AND SALTS; CYTOCHROME P-450 ENZYME SYSTEM; HUMANS; LIVER DISEASES; MODELS, BIOLOGICAL; STEROID HYDROXYLASES; STEROID ISOMERASES; ZELLWEGER SYNDROME;

EID: 0033985195     PISSN: 10935266     EISSN: None     Source Type: Journal    
DOI: 10.1007/s100240050001     Document Type: Review

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