Abnormal bile acid metabolism and neonatal hemochromatosis: A subset with poor prognosis

Journal of Pediatric Gastroenterology and Nutrition

Volumn 25, Issue 3, 1997, Pages 321-326

  Siafakas, Constantinos G ^a   Jonas, Maureen M ^a   Perez Atayde, Antonio R ^b  

^a HARVARD MEDICAL SCHOOL   (United States)

^b BOSTON CHILDREN S HOSPITAL   (United States)

Author keywords

Byler's disease; Congenital cirrhosis; Fast atom bombardment ionization mass spectrometry (FABMS); Gas chromatography and mass spectrometry (GCMS); Neonatal hepatitis

Indexed keywords

7ALPHA HYDROXY 3 OXOCHOL 4 ENOIC ACID; 7ALPHA,12ALPHA DIHYDROXY 3 OXO 4 CHOLENOIC ACID; ACETYLCYSTEINE; ALBUMIN; ALKALINE PHOSPHATASE; AMMONIA; ANTIOXIDANT; BILE ACID; BILE SALT; BILIRUBIN; CHOLIC ACID; D DIMER; DEFEROXAMINE; DIURETIC AGENT; FIBRINOGEN; IRON; PROSTAGLANDIN E; PROTEIN; SELENIUM; STEROID 5BETA REDUCTASE; UNCLASSIFIED DRUG; URSODEOXYCHOLIC ACID;

ARTICLE; ASCITES; BILE ACID METABOLISM; CASE REPORT; CHELATION THERAPY; ELECTRON MICROSCOPY; ENZYME DEFICIENCY; FAST ATOM BOMBARDMENT MASS SPECTROMETRY; FEMALE; GAS CHROMATOGRAPHY; HEMOCHROMATOSIS; HUMAN; HUMAN TISSUE; LIVER BIOPSY; LIVER CIRRHOSIS; LIVER FAILURE; LIVER TRANSPLANTATION; MALE; MASS SPECTROMETRY; NEWBORN; NUCLEAR MAGNETIC RESONANCE IMAGING; ORAL DRUG ADMINISTRATION; PRIORITY JOURNAL; PROGNOSIS;

ADULT; BILE ACIDS AND SALTS; BIOPSY; CHOLESTASIS, INTRAHEPATIC; CHOLIC ACID; CHOLIC ACIDS; FEMALE; GAS CHROMATOGRAPHY-MASS SPECTROMETRY; HEMOCHROMATOSIS; HUMANS; INFANT, NEWBORN; LIVER; LIVER FAILURE; MALE; METABOLISM, INBORN ERRORS; OXIDOREDUCTASES; PROGNOSIS; SPECTROMETRY, MASS, FAST ATOM BOMBARDMENT; URSODEOXYCHOLIC ACID;

EID: 0030766372     PISSN: 02772116     EISSN: None     Source Type: Journal    
DOI: 10.1097/00005176-199709000-00015     Document Type: Article

References (11)

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