Tripeptidyl peptidase I, the late infantile neuronal ceroid lipofuscinosis gene product, initiates the lysosomal degradation of subunit c of ATP synthase

Journal of Biochemistry

Volumn 128, Issue 3, 2000, Pages 509-516

  Ezaki, J ^a   Takeda Ezaki, M ^a   Kominami, E ^a  

^a JUNTENDO UNIVERSITY SCHOOL OF MEDICINE   (Japan)

Author keywords

CLN2; Lysosomes; Neuronal ceroid lipofuscinosis; Subunit c; Tripeptidyl peptidase I

Indexed keywords

GENE PRODUCT; PEPTIDASE; PROTON TRANSPORTING ADENOSINE TRIPHOSPHATASE; TRIPEPTIDYL PEPTIDASE I; UNCLASSIFIED DRUG;

AMINO TERMINAL SEQUENCE; ARTICLE; CONTROLLED STUDY; ENZYME ACTIVITY; ENZYME ANALYSIS; ENZYME DEGRADATION; ENZYME INHIBITION; ENZYME SUBUNIT; FIBROBLAST CULTURE; HUMAN; HUMAN CELL; LYSOSOME; MITOCHONDRION; NEURONAL CEROID LIPOFUSCINOSIS; SPLEEN;

EID: 0033809338     PISSN: 0021924X     EISSN: None     Source Type: Journal    
DOI: 10.1093/oxfordjournals.jbchem.a022781     Document Type: Article

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