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Volumn 28, Issue 1, 1997, Pages 53-55

Decreased lysosomal subunit c-degrading activity in fibroblasts from patients with late infantile neuronal ceroid lipofuscinosis

Author keywords

Batten disease; Proteolysis; Subunit c

Indexed keywords

LYSOSOME ENZYME;

EID: 0030741684     PISSN: 0174304X     EISSN: None     Source Type: Journal    
DOI: 10.1055/s-2007-973668     Document Type: Article
Times cited : (10)

References (12)
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  • 2
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  • 3
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    • Ezaki, J., L. S. Wolfe, E. Kominami: Specific delay in the degradation of mitochondrial ATP synthase subunit c in late infantile neuronal ceroid lipofuscinosis is derived from cellular proteolytic dysfunction rather than structural alteration of subunit c J. Neurochem. 67 (1996) 1677-1687
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  • 6
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    • Characterization of the expressed genes for subunit c of mitochondrial ATP synthase in sheep with ceroid lipofuscinosis
    • Medd, S. M., J. E. Walker, R. D. Jolly: Characterization of the expressed genes for subunit c of mitochondrial ATP synthase in sheep with ceroid lipofuscinosis. Biochem. J. 293 (1993) 65-73
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* 이 정보는 Elsevier사의 SCOPUS DB에서 KISTI가 분석하여 추출한 것입니다.