Biochemical aspects of neuronal ceroid lipofuscinoses

Neurological Sciences

Volumn 21, Issue , 2000, Pages S21-S25

  Tyynela J ^a   Suopanki, J ^a  

^a UNIVERSITY OF HELSINKI   (Finland)

Author keywords

Lysosome; Neurodegeneration; Palmitoyl protein thioesterase; Protein storage; Storage disease; Tripeptidyl peptidase

Indexed keywords

AUTOFLUORESCENCE; AUTOSOMAL RECESSIVE INHERITANCE; BLINDNESS; BRAIN ATROPHY; CELL LOSS; CONFERENCE PAPER; DEATH; DEMENTIA; EPILEPSY; HUMAN; LYSOSOME STORAGE DISEASE; MONOGENIC DISORDER; MOTOR DYSFUNCTION; NERVE CELL DEGENERATION; NEURONAL CEROID LIPOFUSCINOSIS; ONSET AGE;

ENDOPEPTIDASES; HUMAN; LYSOSOMES; NEURONAL CEROID-LIPOFUSCINOSIS; SUPPORT, NON-U.S. GOV'T; THIOLESTER HYDROLASES;

EID: 0033774412     PISSN: 15901874     EISSN: None     Source Type: Journal    
DOI: 10.1007/s100720070036     Document Type: Article

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