Accumulation of sphingolipid activator proteins (SAPs) A and D in granular osmiophilic deposits in miniature Schnauzer dogs with ceroid-lipofuscinosis

Journal of Inherited Metabolic Disease

Volumn 20, Issue 1, 1997, Pages 74-84

  Palmer, D N ^a   Tyynela J ^a,b   Van Mil, H C ^a   Westlake, V J ^c   Jolly, R D ^c  

^a LINCOLN UNIVERSITY   (New Zealand)

^b UNIVERSITY OF HELSINKI   (Finland)

^c MASSEY UNIVERSITY   (New Zealand)

Author keywords

[No Author keywords available]

Indexed keywords

OSMIUM; SPHINGOLIPID ACTIVATOR PROTEIN;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; BRAIN ATROPHY; DEGENERATIVE DISEASE; DOG; GENE MUTATION; IMMUNOBLOTTING; LIPOFUSCINOSIS; NEURONAL CEROID LIPOFUSCINOSIS; NONHUMAN; REVIEW; SEQUENCE ANALYSIS;

ANIMALS; BRAIN; CEREBRAL CORTEX; DOG DISEASES; DOGS; FEMALE; GLYCOPROTEINS; HUMANS; LIVER; MALE; NEURONAL CEROID-LIPOFUSCINOSES; SAPOSINS; SPHINGOLIPID ACTIVATOR PROTEINS;

EID: 0031047001     PISSN: 01418955     EISSN: None     Source Type: Journal    
DOI: 10.1023/A:1005365709340     Document Type: Review

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