Long QT syndrome-associated mutations in the S4-S5 linker of KvLQT1 potassium channels modify gating and interaction with minK subunits

Journal of Biological Chemistry

Volumn 274, Issue 30, 1999, Pages 21063-21070

  Franqueza, Laura ^a   Lin, Monica ^a   Splawski, Igor ^a,c   Keating, Mark T ^a,c   Sanguinetti, Michael C ^a,b  

^a UNIVERSITY OF UTAH SCHOOL OF MEDICINE   (United States)

^b UNIVERSITY OF UTAH   (United States)

^c HOWARD HUGHES MEDICAL INSTITUTE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

POTASSIUM CHANNEL;

ANIMAL CELL; ARTICLE; CARBOXY TERMINAL SEQUENCE; CHANNEL GATING; GENE EXPRESSION; GENE LOCATION; LONG QT SYNDROME; MISSENSE MUTATION; NONHUMAN; POTASSIUM CURRENT; PRIORITY JOURNAL; PROTEIN INTERACTION; QT INTERVAL; VOLTAGE CLAMP;

ANIMALS; ELECTROPHYSIOLOGY; GENE EXPRESSION; HUMANS; ION CHANNEL GATING; KCNQ POTASSIUM CHANNELS; KCNQ1 POTASSIUM CHANNEL; LONG QT SYNDROME; MUTATION; POTASSIUM CHANNELS; POTASSIUM CHANNELS, VOLTAGE-GATED; XENOPUS;

AMPHIBIA; ANIMALIA; MUSTELA VISON; REPTILIA;

EID: 0033597857     PISSN: 00219258     EISSN: None     Source Type: Journal    
DOI: 10.1074/jbc.274.30.21063     Document Type: Article

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