Properties of KvLQT1 K+ channel mutations in Romano-Ward and Jervell and Lange-Nielsen inherited cardiac arrhythmias

EMBO Journal

Volumn 16, Issue 17, 1997, Pages 5472-5479

  Chouabe, Christophe ^a   Neyroud, Nathalie ^b   Guicheney, Pascale ^b   Lazdunski, Michel ^a   Romey, Georges ^a   Barhanin, Jacques ^a  

^a CNRS   (France)

^b PITIÉ SALPÊTRIÈRE HOSPITAL   (France)

Author keywords

Delayed rectifier; Dominant negative; I(Ks); IsK; Long QT MinK

Indexed keywords

POTASSIUM CHANNEL; POTASSIUM ION; PROTEIN SUBUNIT;

ADULT; ANIMAL CELL; ARTICLE; CYTOPLASM; DOMINANT GENE; GENE EXPRESSION; GENE MUTATION; HEART; HUMAN; HUMAN TISSUE; LONG QT SYNDROME; MOLECULAR CLONING; NONHUMAN; POTASSIUM CURRENT; PRIORITY JOURNAL; PROTEIN PROTEIN INTERACTION; PROTEIN STRUCTURE; PROTEIN VARIANT; TISSUE DISTRIBUTION;

AMINO ACID SEQUENCE; ANIMALS; CLONING, MOLECULAR; COS CELLS; DNA, COMPLEMENTARY; ELECTROPHYSIOLOGY; HUMANS; KCNQ POTASSIUM CHANNELS; KCNQ1 POTASSIUM CHANNEL; LONG QT SYNDROME; MODELS, MOLECULAR; MOLECULAR SEQUENCE DATA; MUTAGENESIS, SITE-DIRECTED; MUTATION; PHENOTYPE; POTASSIUM CHANNELS; POTASSIUM CHANNELS, VOLTAGE-GATED; RECOMBINANT PROTEINS; SEQUENCE ANALYSIS, DNA; SEQUENCE HOMOLOGY, AMINO ACID; TISSUE DISTRIBUTION;

ANIMALIA; MUSTELA VISON;

EID: 0030799943     PISSN: 02614189     EISSN: None     Source Type: Journal    
DOI: 10.1093/emboj/16.17.5472     Document Type: Article

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