Biochemical and molecular aspects of genetic disorders of bilirubin metabolism

Biochimica et Biophysica Acta - Molecular Basis of Disease

Volumn 1407, Issue 3, 1998, Pages 173-184

  Iyanagi, Takashi ^a   Emi, Yoshikazu ^a   Ikushiro, Shin Ichi ^a  

^a UNIVERSITY OF HYOGO   (Japan)

Author keywords

Bilirubin; Crigler Najjar syndrome; Dubin Johnson syndrome; Gene therapy; Gunn rat; GY TR rat; Hyperbilirubinemia; Multidrug resistance protein 2; UDP glucuronosyltransferase

Indexed keywords

BILIRUBIN; BILIRUBIN GLUCURONIDE; GLUCURONOSYLTRANSFERASE;

ANIMAL MODEL; BILIRUBIN METABOLISM; CRIGLER NAJJAR SYNDROME; DUBIN JOHNSON SYNDROME; ENZYME ACTIVITY; GENE MUTATION; GENE THERAPY; GENETIC ANALYSIS; GILBERT DISEASE; GLUCURONIDATION; HUMAN; HYPERBILIRUBINEMIA; LIVER MICROSOME; NONHUMAN; PRIORITY JOURNAL; RAT; REVIEW;

ANIMALS; ANION TRANSPORT PROTEINS; BILE; BILIRUBIN; CARRIER PROTEINS; DISEASE MODELS, ANIMAL; GLUCURONOSYLTRANSFERASE; HEME; HUMANS; HYPERBILIRUBINEMIA, HEREDITARY; RATS; RATS, GUNN;

ANIMALIA; MAMMALIA; RATTUS NORVEGICUS;

EID: 0032413678     PISSN: 09254439     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0925-4439(98)00044-1     Document Type: Review

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