Leber hereditary optic neuropathy: Respiratory chain dysfunction and degeneration of the optic nerve

Vision Research

Volumn 38, Issue 10, 1998, Pages 1495-1504

  Howell, Neil ^a  

^a Biology Division 0656   (United States)

Author keywords

Bioenergetics; Ganglion cell layer; Leber hereditary optic neuropathy; Mitochondrial genetics; Neurodegeneration; Optic nerve disorders

Indexed keywords

MITOCHONDRIAL DNA;

CONFERENCE PAPER; GENE MUTATION; HEREDITARY OPTIC ATROPHY; OPTIC NERVE ATROPHY; PRIORITY JOURNAL; RESPIRATORY CHAIN; RETINA GANGLION CELL; VISUAL IMPAIRMENT;

CELL DEATH; DNA, MITOCHONDRIAL; ELECTRON TRANSPORT; FEMALE; HUMANS; MALE; MODELS, NEUROLOGICAL; MUTATION; NERVE DEGENERATION; OPTIC ATROPHIES, HEREDITARY; OPTIC NERVE; PENETRANCE; RETINAL GANGLION CELLS;

EID: 0032078333     PISSN: 00426989     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0042-6989(97)00444-6     Document Type: Conference Paper

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