Spinobulbar muscular atrophy: Polyglutamine-expanded androgen receptor is proteolytically resistant in vitro and processed abnormally in transfected cells

Human Molecular Genetics

Volumn 7, Issue 3, 1998, Pages 379-384

  Abdullah, Abdullah A R ^a,b   Trifiro, Mark A ^a,b   Panet Raymond, Valerie ^a,b   Alvarado, Carlos ^a   De Tourreil, Sunita ^a,b   Frankel, Dov ^a,b   Schipper, Hyman M ^a,b   Pinsky, Leonard ^a,b  

^a MCGILL UNIVERSITY   (Canada)

^b MCGILL UNIVERSITY   (Canada)

Author keywords

[No Author keywords available]

Indexed keywords

ANDROGEN RECEPTOR; COMPLEMENTARY DNA; GLUTAMINE; UREA;

ANIMAL CELL; APOPTOSIS; ARTICLE; CELL STRAIN COS1; CONTROLLED STUDY; DNA TRANSFECTION; MUSCLE ATROPHY; NEUROTOXICITY; NONHUMAN; PRIORITY JOURNAL; PROTEIN DEGRADATION; PROTEIN PROCESSING; PROTEIN STABILITY; TRINUCLEOTIDE REPEAT;

ANIMALS; CELL SURVIVAL; COS CELLS; HUMANS; MUSCULAR ATROPHY, SPINAL; PEPTIDES; PROTEIN BIOSYNTHESIS; RABBITS; RECEPTORS, ANDROGEN; RECOMBINANT PROTEINS; RETICULOCYTES; TRANSCRIPTION, GENETIC; TRANSFECTION; TRINUCLEOTIDE REPEATS; ULTRAVIOLET RAYS;

EID: 0031934542     PISSN: 09646906     EISSN: None     Source Type: Journal    
DOI: 10.1093/hmg/7.3.379     Document Type: Article

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