Strategies for correcting the ΔF508 CFTR protein-folding defect

Journal of Bioenergetics and Biomembranes

Volumn 29, Issue 5, 1997, Pages 491-502

  Brown, C Randell ^a   Hong Brown, Ly Q ^a   Welch, William J ^a  

^a UNIVERSITY OF CALIFORNIA   (United States)

Author keywords

Chemical chaperones; Cystic fibrosis; Glycerol; Osmolytes; Protein folding; Temperature sensitive

Indexed keywords

CHLORIDE CHANNEL; TRANSMEMBRANE CONDUCTANCE REGULATOR;

AMINO ACID SEQUENCE; CYSTIC FIBROSIS; GENE THERAPY; HUMAN; PROTEIN CONFORMATION; PROTEIN FOLDING; PROTEIN SYNTHESIS; SHORT SURVEY; TEMPERATURE SENSITIVITY;

AMINOGLYCOSIDES; ANTI-BACTERIAL AGENTS; CYSTIC FIBROSIS; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; GENE THERAPY; HUMANS; MOLECULAR CHAPERONES; MUTATION; PROTEIN FOLDING;

EID: 0031425079     PISSN: 0145479X     EISSN: None     Source Type: Journal    
DOI: 10.1023/A:1022491124939     Document Type: Short Survey

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