Nuclear DNA-encoded tRNAs targeted into mitochondria can rescue a mitochondrial DNA mutation associated with the MERRF syndrome in cultured human cells

Human Molecular Genetics

Volumn 13, Issue 20, 2004, Pages 2519-2534

  Kolesnikova, Olga A ^a,b,c   Entelis, Nina S ^a   Jacquin Becker, Clarisse ^a   Goltzene, Francine ^a   Chrzanowska Lightowlers, Zofia M ^c   Lightowlers, Robert N ^c   Martin, Robert P ^a   Tarassov, Ivan ^a  

^a UNIVERSITÉ DE STRASBOURG   (France)

^b MOSCOW STATE UNIVERSITY   (Russian Federation)

^c NEWCASTLE UNIVERSITY   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

ADENINE; CELL NUCLEUS DNA; GUANINE; LYSINE; LYSINE TRANSFER RNA; MITOCHONDRIAL DNA; SMALL INTERFERING RNA; TRANSFER RNA; VIRUS VECTOR;

AMINOACYLATION; ANTICODON; ARTICLE; CELL CULTURE; CELL IMMORTALIZATION; CONTROLLED STUDY; CYTOMEGALOVIRUS; CYTOSOL; DISORDERS OF MITOCHONDRIAL FUNCTIONS; DOWN REGULATION; ELECTROCHEMICAL ANALYSIS; FIBROBLAST; GENE MUTATION; GENETIC ASSOCIATION; HUMAN; HUMAN CELL; HYBRID CELL; IN VIVO STUDY; MERRF SYNDROME; MITOCHONDRIAL MEMBRANE; MITOCHONDRIAL RESPIRATION; MITOCHONDRION; PATHOGENESIS; PRIORITY JOURNAL; PROTEIN TARGETING; RNA TRANSLATION; RNA TRANSPORT;

ANTICODON; CELL NUCLEUS; CELLS, CULTURED; CYTOPLASM; DNA; DNA, MITOCHONDRIAL; ELECTRON TRANSPORT COMPLEX IV; FIBROBLASTS; HUMANS; MERRF SYNDROME; MITOCHONDRIA; MUTATION; PROTEIN BIOSYNTHESIS; RNA TRANSPORT; RNA, SMALL INTERFERING; RNA, TRANSFER, LYS; SACCHAROMYCES CEREVISIAE;

ANIMALIA; FUNGI; PROTOZOA;

EID: 9644264375     PISSN: 09646906     EISSN: None     Source Type: Journal    
DOI: 10.1093/hmg/ddh267     Document Type: Article

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