A Panel of Slow-Channel Syndrome Mice Reveals a Unique Locomotor Behavioral Signature

Journal of Neuromuscular Diseases

Volumn 4, Issue 4, 2017, Pages 341-347

  Grajales Reyes, José G ^a,c   García González, Aurian ^a,d   María Ríos, José C ^a   Grajales Reyes, Gary E ^a,c   Delgado Vélez, Manuel ^a   Báez Pagán, Carlos A ^a   Quesada, Orestes ^a   Gómez, Christopher M ^b   Lasalde Dominicci, José A ^a  

^a UNIVERSITY OF PUERTO RICO   (Puerto Rico)

^b UNIVERSITY OF CHICAGO   (United States)

^c WASHINGTON UNIVERSITY SCHOOL OF MEDICINE   (United States)

^d UNIVERSITY OF MASSACHUSETTS MEDICAL SCHOOL   (United States)

Author keywords

acetylcholine; Congenital myasthenia; locomotor activity; mice; motor endplate; myalgia; neuromuscular junction (NMJ); nicotinic acetylcholine receptor (nAChR); running

Indexed keywords

MUTANT PROTEIN; NICOTINIC RECEPTOR;

ALPHAC418W GENE; ALPHAL251T GENE; ALPHAV249F GENE; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; BREATHING RATE; C57BL 6 MOUSE; CALCIFICATION; CONGENITAL MYASTHENIC SYNDROME; CONTROLLED STUDY; DELTAS262T GENE; DELTAS268F GENE; FVB/N MOUSE; GENE MUTATION; GENETIC DISTANCE; GRIP STRENGTH; INFANT; LOCOMOTION; MALE; MOUSE; MUSCLE WEAKNESS; NACHR GENE; NEUROMUSCULAR JUNCTION; NONHUMAN; PATHOPHYSIOLOGY; PHENOTYPE; PRIORITY JOURNAL; RUNNING; VELOCITY; ANIMAL; C57BL MOUSE; COGNITION; DISEASE MODEL; GAIT; GENETICS; METABOLISM; MOTOR DYSFUNCTION; MULTIVARIATE ANALYSIS; MUTATION; PHYSIOLOGY; SPECIES DIFFERENCE; SYNDROME; TRANSGENIC MOUSE;

ANIMALS; DISEASE MODELS, ANIMAL; GAIT ANALYSIS; LOCOMOTION; MALE; MICE, INBRED C57BL; MICE, TRANSGENIC; MOVEMENT DISORDERS; MULTIVARIATE ANALYSIS; MUTATION; PHENOTYPE; RECEPTORS, NICOTINIC; SPECIES SPECIFICITY; SYNDROME; VOLITION;

EID: 85041164832     PISSN: 22143599     EISSN: 22143602     Source Type: Journal    
DOI: 10.3233/JND-170226     Document Type: Article

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