A cluster of palmitoylated cysteines are essential for aggregation of cysteine-string protein mutants that cause neuronal ceroid lipofuscinosis

Scientific Reports

Volumn 7, Issue 1, 2017, Pages

  Diez Ardanuy, Cinta ^a   Greaves, Jennifer ^a   Munro, Kevin R ^a   Tomkinson, Nicholas C O ^a   Chamberlain, Luke H ^a  

^a UNIVERSITY OF STRATHCLYDE   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

CYSTEINE; CYSTEINE STRING PROTEIN; HEAT SHOCK PROTEIN 40; MEMBRANE PROTEIN;

GENE DELETION; GENETICS; HUMAN; LIPOYLATION; METABOLISM; MISSENSE MUTATION; NEURONAL CEROID LIPOFUSCINOSIS; PATHOLOGY; PROTEIN PROCESSING; PROTEINOSIS;

CYSTEINE; HSP40 HEAT-SHOCK PROTEINS; HUMANS; LIPOYLATION; MEMBRANE PROTEINS; MUTATION, MISSENSE; NEURONAL CEROID-LIPOFUSCINOSES; PROTEIN AGGREGATION, PATHOLOGICAL; PROTEIN PROCESSING, POST-TRANSLATIONAL; SEQUENCE DELETION;

EID: 85017963868     PISSN: None     EISSN: 20452322     Source Type: Journal    
DOI: 10.1038/s41598-017-00036-8     Document Type: Article

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