Oligomerization of Cysteine String Protein alpha mutants causing adult neuronal ceroid lipofuscinosis

Biochimica et Biophysica Acta - Molecular Basis of Disease

Volumn 1842, Issue 11, 2014, Pages

  Zhang, Yong quan ^a   Chandra, Sreeganga S ^a,b  

^a YALE UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b YALE UNIVERSITY   (United States)

Author keywords

ATPase; Heat shock cognate; Lysosomal storage disease; Synapse maintenance

Indexed keywords

CHAPERONE; CYSTEINE STRING PROTEIN; CYSTEINE STRING PROTEIN ALPHA; MUTANT PROTEIN; UNCLASSIFIED DRUG;

ADULT; ANIMAL EXPERIMENT; ARTICLE; CONCENTRATION (PARAMETERS); ESCHERICHIA COLI; HEK293 CELL LINE; MOLECULAR RECOGNITION; MOUSE; NEURONAL CEROID LIPOFUSCINOSIS; NEUROPATHOLOGY; NONHUMAN; OLIGOMERIZATION; PALMITOYLATION; PROTEIN ANALYSIS; PROTEIN FUNCTION; PROTEIN PURIFICATION; TEMPERATURE; TIME; UBIQUITINATION;

EID: 84908078138     PISSN: 09254439     EISSN: 1879260X     Source Type: Journal    
DOI: 10.1016/j.bbadis.2014.07.009     Document Type: Article

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