Myocardial fibrosis burden predicts left ventricular ejection fraction and is associated with age and steroid treatment duration in duchenne muscular dystrophy

Journal of the American Heart Association

Volumn 4, Issue 4, 2015, Pages

  Tandon, Animesh ^a   Villa, Chet R ^a   Hor, Kan N ^d,e   Jefferies, John L ^a   Gao, Zhiqian ^a   Towbin, Jeffrey A ^a   Wong, Brenda L ^b   Mazur, Wojciech ^f   Fleck, Robert J ^c   Sticka, Joshua J ^a   Benson, D Woodrow ^g   Taylor, Michael D ^a  

^a HEART INSTITUTE   (United States)

^b Division of Neurology   (United States)

^c Division of Radiology   (United States)

^d CINCINNATI CHILDREN'S HOSPITAL MEDICAL CENTER   (United States)

^e NATIONWIDE CHILDREN S HOSPITAL   (United States)

^f CHRIST HOSPITAL   (United States)

^g Children's Hospital of Wisconsin   (United States)

Author keywords

Cardiomyopathy; Magnetic resonance imaging; Morbidity

Indexed keywords

DEFLAZACORT; GADOLINIUM; PREDNISONE; GLUCOCORTICOID; PREGNANE DERIVATIVE;

AGE; ARTICLE; CARDIOVASCULAR MAGNETIC RESONANCE; COHORT ANALYSIS; CONTRAST ENHANCEMENT; CONTROLLED STUDY; DISEASE ASSOCIATION; DUCHENNE MUSCULAR DYSTROPHY; HEART LEFT VENTRICLE EJECTION FRACTION; HEART MUSCLE FIBROSIS; HOLTER MONITORING; HUMAN; LONGITUDINAL STUDY; MALE; RETROSPECTIVE STUDY; TREATMENT DURATION; VECTORCARDIOGRAPHY; ADOLESCENT; ADULT; CARDIAC MUSCLE; CHILD; COMPLICATION; DISEASE COURSE; DRUG EFFECTS; FIBROSIS; HEART; HEART STROKE VOLUME; MUSCULAR DYSTROPHY, DUCHENNE; NUCLEAR MAGNETIC RESONANCE IMAGING; PATHOLOGY; PATHOPHYSIOLOGY; PHYSIOLOGY; YOUNG ADULT;

ADOLESCENT; ADULT; AGE FACTORS; CHILD; DISEASE PROGRESSION; FIBROSIS; GLUCOCORTICOIDS; HEART; HUMANS; MAGNETIC RESONANCE IMAGING; MALE; MUSCULAR DYSTROPHY, DUCHENNE; MYOCARDIUM; PREDNISONE; PREGNENEDIONES; RETROSPECTIVE STUDIES; STROKE VOLUME; YOUNG ADULT;

EID: 85012285866     PISSN: None     EISSN: 20479980     Source Type: Journal    
DOI: 10.1161/JAHA.114.001338     Document Type: Article

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