-
1
-
-
80955131827
-
Lung clearance index: clinical and research applications in children
-
1 Fuchs, S.I., Gappa, M., Lung clearance index: clinical and research applications in children. Paediatr Respir Rev 12:4 (2011), 264–270.
-
(2011)
Paediatr Respir Rev
, vol.12
, Issue.4
, pp. 264-270
-
-
Fuchs, S.I.1
Gappa, M.2
-
2
-
-
84895069609
-
Lung clearance index: evidence for use in clinical trials in cystic fibrosis
-
2 Kent, L., Reix, P., Innes, J.A., et al. Lung clearance index: evidence for use in clinical trials in cystic fibrosis. J Cyst Fibros 13:2 (2014), 123–138.
-
(2014)
J Cyst Fibros
, vol.13
, Issue.2
, pp. 123-138
-
-
Kent, L.1
Reix, P.2
Innes, J.A.3
-
3
-
-
84860110054
-
Early cystic fibrosis lung disease detected by bronchoalveolar lavage and lung clearance index
-
3 Belessis, Y., Dixon, B., Hawkins, G., et al. Early cystic fibrosis lung disease detected by bronchoalveolar lavage and lung clearance index. Am J Respir Crit Care Med 185:8 (2012), 862–873.
-
(2012)
Am J Respir Crit Care Med
, vol.185
, Issue.8
, pp. 862-873
-
-
Belessis, Y.1
Dixon, B.2
Hawkins, G.3
-
4
-
-
9644259076
-
Multiple breath inert gas washout as a measure of ventilation distribution in children with cystic fibrosis
-
4 Aurora, P., Gustafsson, P., Bush, A., et al. Multiple breath inert gas washout as a measure of ventilation distribution in children with cystic fibrosis. Thorax 59:12 (2004), 1068–1073.
-
(2004)
Thorax
, vol.59
, Issue.12
, pp. 1068-1073
-
-
Aurora, P.1
Gustafsson, P.2
Bush, A.3
-
5
-
-
84881381613
-
Practicability of nitrogen multiple-breath washout measurements in a pediatric cystic fibrosis outpatient setting
-
5 Singer, F., Kieninger, E., Abbas, C., et al. Practicability of nitrogen multiple-breath washout measurements in a pediatric cystic fibrosis outpatient setting. Pediatr Pulmonol 48:8 (2013), 739–746.
-
(2013)
Pediatr Pulmonol
, vol.48
, Issue.8
, pp. 739-746
-
-
Singer, F.1
Kieninger, E.2
Abbas, C.3
-
6
-
-
77951988740
-
Hypertonic saline improves the LCI in paediatric patients with CF with normal lung function
-
6 Amin, R., Subbarao, P., Jabar, A., et al. Hypertonic saline improves the LCI in paediatric patients with CF with normal lung function. Thorax 65:5 (2010), 379–383.
-
(2010)
Thorax
, vol.65
, Issue.5
, pp. 379-383
-
-
Amin, R.1
Subbarao, P.2
Jabar, A.3
-
7
-
-
79956360940
-
Lung clearance index and HRCT are complementary markers of lung abnormalities in young children with CF
-
7 Owens, C.M., Aurora, P., Stanojevic, S., et al. Lung clearance index and HRCT are complementary markers of lung abnormalities in young children with CF. Thorax 66:6 (2011), 481–488.
-
(2011)
Thorax
, vol.66
, Issue.6
, pp. 481-488
-
-
Owens, C.M.1
Aurora, P.2
Stanojevic, S.3
-
8
-
-
39049084491
-
Multiple-breath inert gas washout and spirometry versus structural lung disease in cystic fibrosis
-
8 Gustafsson, P.M., De Jong, P.A., Tiddens, H.A., Lindblad, A., Multiple-breath inert gas washout and spirometry versus structural lung disease in cystic fibrosis. Thorax 63:2 (2008), 129–134.
-
(2008)
Thorax
, vol.63
, Issue.2
, pp. 129-134
-
-
Gustafsson, P.M.1
De Jong, P.A.2
Tiddens, H.A.3
Lindblad, A.4
-
9
-
-
80051850244
-
Air trapping on chest CT is associated with worse ventilation distribution in infants with cystic fibrosis diagnosed following newborn screening
-
9 Hall, G.L., Logie, K.M., Parsons, F., et al. Air trapping on chest CT is associated with worse ventilation distribution in infants with cystic fibrosis diagnosed following newborn screening. PLoS One, 6(8), 2011, e23932.
-
(2011)
PLoS One
, vol.6
, Issue.8
, pp. e23932
-
-
Hall, G.L.1
Logie, K.M.2
Parsons, F.3
-
10
-
-
84866070431
-
Lung function is abnormal in 3-month-old infants with cystic fibrosis diagnosed by newborn screening
-
10 Hoo, A.F., Thia, L.P., Nguyen, T.T.D., et al. Lung function is abnormal in 3-month-old infants with cystic fibrosis diagnosed by newborn screening. Thorax 67:10 (2012), 874–881.
-
(2012)
Thorax
, vol.67
, Issue.10
, pp. 874-881
-
-
Hoo, A.F.1
Thia, L.P.2
Nguyen, T.T.D.3
-
11
-
-
79952504576
-
Lung clearance index at 4 years predicts subsequent lung function in children with cystic fibrosis
-
11 Aurora, P., Stanojevic, S., Wade, A., et al. Lung clearance index at 4 years predicts subsequent lung function in children with cystic fibrosis. Am J Respir Crit Care Med 183:6 (2011), 752–758.
-
(2011)
Am J Respir Crit Care Med
, vol.183
, Issue.6
, pp. 752-758
-
-
Aurora, P.1
Stanojevic, S.2
Wade, A.3
-
12
-
-
12744277962
-
Multiple-breath washout as a marker of lung disease in preschool children with cystic fibrosis
-
12 Aurora, P., Bush, A., Gustafsson, P., et al. Multiple-breath washout as a marker of lung disease in preschool children with cystic fibrosis. Am J Respir Crit Care Med 171:3 (2005), 249–256.
-
(2005)
Am J Respir Crit Care Med
, vol.171
, Issue.3
, pp. 249-256
-
-
Aurora, P.1
Bush, A.2
Gustafsson, P.3
-
13
-
-
0346121620
-
Evaluation of ventilation maldistribution as an early indicator of lung disease in children with cystic fibrosis
-
13 Gustafsson, P.M., Aurora, P., Lindblad, A., Evaluation of ventilation maldistribution as an early indicator of lung disease in children with cystic fibrosis. Eur Respir J 22:6 (2003), 972–979.
-
(2003)
Eur Respir J
, vol.22
, Issue.6
, pp. 972-979
-
-
Gustafsson, P.M.1
Aurora, P.2
Lindblad, A.3
-
14
-
-
77951983616
-
Multiple-breath inert gas washout test and early cystic fibrosis lung disease
-
14 Aurora, P., Multiple-breath inert gas washout test and early cystic fibrosis lung disease. Thorax 65:5 (2010), 373–374.
-
(2010)
Thorax
, vol.65
, Issue.5
, pp. 373-374
-
-
Aurora, P.1
-
15
-
-
84890309789
-
Lung clearance index predicts pulmonary exacerbations in young patients with cystic fibrosis
-
15 Vermeulen, F., Proesmans, M., Boon, M., Havermans, T., De Boeck, K., Lung clearance index predicts pulmonary exacerbations in young patients with cystic fibrosis. Thorax 69:1 (2014), 39–45.
-
(2014)
Thorax
, vol.69
, Issue.1
, pp. 39-45
-
-
Vermeulen, F.1
Proesmans, M.2
Boon, M.3
Havermans, T.4
De Boeck, K.5
-
16
-
-
84882662774
-
Lung clearance index as an outcome measure for clinical trials in young children with cystic fibrosis. A pilot study using inhaled hypertonic saline
-
16 Subbarao, P., Stanojevic, S., Brown, M., et al. Lung clearance index as an outcome measure for clinical trials in young children with cystic fibrosis. A pilot study using inhaled hypertonic saline. Am J Respir Crit Care Med 188:4 (2013), 456–460.
-
(2013)
Am J Respir Crit Care Med
, vol.188
, Issue.4
, pp. 456-460
-
-
Subbarao, P.1
Stanojevic, S.2
Brown, M.3
-
17
-
-
79953287790
-
The effect of dornase alfa on ventilation inhomogeneity in patients with cystic fibrosis
-
17 Amin, R., Subbarao, P., Lou, W., et al. The effect of dornase alfa on ventilation inhomogeneity in patients with cystic fibrosis. Eur Respir J 37:4 (2011), 806–812.
-
(2011)
Eur Respir J
, vol.37
, Issue.4
, pp. 806-812
-
-
Amin, R.1
Subbarao, P.2
Lou, W.3
-
18
-
-
84885071273
-
Assessment of clinical response to ivacaftor with lung clearance index in cystic fibrosis patients with a G551D-CFTR mutation and preserved spirometry: a randomised controlled trial
-
18 Davies, J., Sheridan, H., Bell, N., et al. Assessment of clinical response to ivacaftor with lung clearance index in cystic fibrosis patients with a G551D-CFTR mutation and preserved spirometry: a randomised controlled trial. Lancet Respir Med 1:8 (2013), 630–638.
-
(2013)
Lancet Respir Med
, vol.1
, Issue.8
, pp. 630-638
-
-
Davies, J.1
Sheridan, H.2
Bell, N.3
-
19
-
-
39049105720
-
Lung clearance index is a sensitive, repeatable and practical measure of airways disease in adults with cystic fibrosis
-
19 Horsley, A.R., Gustafsson, P.M., Macleod, K.A., et al. Lung clearance index is a sensitive, repeatable and practical measure of airways disease in adults with cystic fibrosis. Thorax 63:2 (2008), 135–140.
-
(2008)
Thorax
, vol.63
, Issue.2
, pp. 135-140
-
-
Horsley, A.R.1
Gustafsson, P.M.2
Macleod, K.A.3
-
20
-
-
84882683258
-
Lung clearance index in adult cystic fibrosis patients: the role of convection-dependent lung units
-
20 Verbanck, S., Paiva, M., Paeps, E., et al. Lung clearance index in adult cystic fibrosis patients: the role of convection-dependent lung units. Eur Respir J 42:2 (2013), 380–388.
-
(2013)
Eur Respir J
, vol.42
, Issue.2
, pp. 380-388
-
-
Verbanck, S.1
Paiva, M.2
Paeps, E.3
-
21
-
-
84902279305
-
Tracking lung clearance index and chest CT in mild cystic fibrosis lung disease over a period of three years
-
21 Fuchs, S.I., Gappa, M., Eder, J., Unsinn, K.M., Steinkamp, G., Ellemunter, H., Tracking lung clearance index and chest CT in mild cystic fibrosis lung disease over a period of three years. Respir Med 108:6 (2014), 865–874.
-
(2014)
Respir Med
, vol.108
, Issue.6
, pp. 865-874
-
-
Fuchs, S.I.1
Gappa, M.2
Eder, J.3
Unsinn, K.M.4
Steinkamp, G.5
Ellemunter, H.6
-
22
-
-
78650016662
-
Sensitivity of Lung clearance index and chest computed tomography in early CF lung disease
-
22 Ellemunter, H., Fuchs, S.I., Unsinn, K.M., et al. Sensitivity of Lung clearance index and chest computed tomography in early CF lung disease. Respir Med 104:12 (2010), 1834–1842.
-
(2010)
Respir Med
, vol.104
, Issue.12
, pp. 1834-1842
-
-
Ellemunter, H.1
Fuchs, S.I.2
Unsinn, K.M.3
-
23
-
-
34548288533
-
An overview of endpoints for cystic fibrosis clinical trials: one size does not fit all
-
23 Rosenfeld, M., An overview of endpoints for cystic fibrosis clinical trials: one size does not fit all. Proc Am Thorac Soc 4:4 (2007), 299–301.
-
(2007)
Proc Am Thorac Soc
, vol.4
, Issue.4
, pp. 299-301
-
-
Rosenfeld, M.1
-
24
-
-
79955644127
-
Cystic fibrosis and survival to 40 years: a study of cystic fibrosis transmembrane conductance regulator function
-
24 Simmonds, N.J., D'Souza, L., Roughton, M., Alton, E.W., Davies, J.C., Hodson, M.E., Cystic fibrosis and survival to 40 years: a study of cystic fibrosis transmembrane conductance regulator function. Eur Respir J 37:5 (2011), 1076–1082.
-
(2011)
Eur Respir J
, vol.37
, Issue.5
, pp. 1076-1082
-
-
Simmonds, N.J.1
D'Souza, L.2
Roughton, M.3
Alton, E.W.4
Davies, J.C.5
Hodson, M.E.6
-
25
-
-
84942254217
-
Multiple-breath washout as a lung function test in cystic fibrosis. A Cystic Fibrosis Foundation workshop report
-
25 Subbarao, P., Milla, C., Aurora, P., et al. Multiple-breath washout as a lung function test in cystic fibrosis. A Cystic Fibrosis Foundation workshop report. Ann Am Thorac Soc 12:6 (2015), 932–939.
-
(2015)
Ann Am Thorac Soc
, vol.12
, Issue.6
, pp. 932-939
-
-
Subbarao, P.1
Milla, C.2
Aurora, P.3
-
26
-
-
50849128461
-
Effects of cystic fibrosis lung disease on gas mixing indices derived from alveolar slope analysis
-
26 Horsley, A.R., Macleod, K.A., Robson, A.G., et al. Effects of cystic fibrosis lung disease on gas mixing indices derived from alveolar slope analysis. Respir Physiol Neurobiol 162:3 (2008), 197–203.
-
(2008)
Respir Physiol Neurobiol
, vol.162
, Issue.3
, pp. 197-203
-
-
Horsley, A.R.1
Macleod, K.A.2
Robson, A.G.3
-
27
-
-
85069371443
-
S44 Lung clearance index (LCI) and FEV1 correlate equally with treatment burden as measured by cystic fibrosis questionnaire-revised (CFQ-R)
-
27 O'Neill, K., Bradley, J.M., Tunney, M., Elborn, J.S., S44 Lung clearance index (LCI) and FEV1 correlate equally with treatment burden as measured by cystic fibrosis questionnaire-revised (CFQ-R). Thorax, 66, 2011, A23.
-
(2011)
Thorax
, vol.66
, pp. A23
-
-
O'Neill, K.1
Bradley, J.M.2
Tunney, M.3
Elborn, J.S.4
-
28
-
-
85002785290
-
159 lung clearance index (LCI) during and following a pulmonary exacerbation (PEx) in patients with CF
-
28 O'Neill, K., Johnston, E., Tunney, M., Elborn, J.S., Bradley, J.M., 159 lung clearance index (LCI) during and following a pulmonary exacerbation (PEx) in patients with CF. J Cyst Fibros, 11, 2012, S97.
-
(2012)
J Cyst Fibros
, vol.11
, pp. S97
-
-
O'Neill, K.1
Johnston, E.2
Tunney, M.3
Elborn, J.S.4
Bradley, J.M.5
-
29
-
-
85002928428
-
WS7.3 relationships between lung clearance index (LCI), patient reported symptoms and health related quality of life (HRQoL) in CF
-
29 O'Neill, K., Johnston, E., Tunney, M., Elborn, J.S., Bradley, J.M., WS7.3 relationships between lung clearance index (LCI), patient reported symptoms and health related quality of life (HRQoL) in CF. J Cyst Fibros, 11, 2012, S14.
-
(2012)
J Cyst Fibros
, vol.11
, pp. S14
-
-
O'Neill, K.1
Johnston, E.2
Tunney, M.3
Elborn, J.S.4
Bradley, J.M.5
-
30
-
-
0031900652
-
The diagnosis of cystic fibrosis: A consensus statement
-
30 Rosenstein, B.J., Cutting, G.R., The diagnosis of cystic fibrosis: A consensus statement. J Pediatr 132:4 (1998), 589–595.
-
(1998)
J Pediatr
, vol.132
, Issue.4
, pp. 589-595
-
-
Rosenstein, B.J.1
Cutting, G.R.2
-
31
-
-
21744460289
-
Standardisation of spirometry
-
31 Miller, M.R., Hankinson, J., Brusasco, V., et al. Standardisation of spirometry. Eur Respir J 26:2 (2005), 319–338.
-
(2005)
Eur Respir J
, vol.26
, Issue.2
, pp. 319-338
-
-
Miller, M.R.1
Hankinson, J.2
Brusasco, V.3
-
32
-
-
38849129311
-
Reference ranges for spirometry across all ages
-
32 Stanojevic, S., Wade, A., Stocks, J., et al. Reference ranges for spirometry across all ages. Am J Respir Crit Care Med 177:3 (2008), 253–260.
-
(2008)
Am J Respir Crit Care Med
, vol.177
, Issue.3
, pp. 253-260
-
-
Stanojevic, S.1
Wade, A.2
Stocks, J.3
-
33
-
-
84960126903
-
A randomized controlled trial to evaluate the lung clearance index as an outcome measure for early phase studies in patients with cystic fibrosis
-
33 Amin, R., Stanojevic, S., Kane, M., Webster, H., Ratjen, F., A randomized controlled trial to evaluate the lung clearance index as an outcome measure for early phase studies in patients with cystic fibrosis. Respir Med 112 (2016), 59–64.
-
(2016)
Respir Med
, vol.112
, pp. 59-64
-
-
Amin, R.1
Stanojevic, S.2
Kane, M.3
Webster, H.4
Ratjen, F.5
-
34
-
-
0033635739
-
A permutation test to compare receiver operating characteristic curves
-
34 Venkatraman, E.S., A permutation test to compare receiver operating characteristic curves. Biometrics 56:4 (2000), 1134–1138.
-
(2000)
Biometrics
, vol.56
, Issue.4
, pp. 1134-1138
-
-
Venkatraman, E.S.1
-
35
-
-
0038102859
-
Evaluation of a new definition for chronic Pseudomonas aeruginosa infection in cystic fibrosis patients
-
35 Lee, T.W.R., Brownlee, K.G., Conway, S.P., Denton, M., Littlewood, J.M., Evaluation of a new definition for chronic Pseudomonas aeruginosa infection in cystic fibrosis patients. J Cystic Fibrosis 2:1 (2003), 29–34.
-
(2003)
J Cystic Fibrosis
, vol.2
, Issue.1
, pp. 29-34
-
-
Lee, T.W.R.1
Brownlee, K.G.2
Conway, S.P.3
Denton, M.4
Littlewood, J.M.5
-
36
-
-
84908219488
-
Statistical methods for assessing agreement between two methods of clinical measurement
-
36 Bland, J.M., Altman, D.G., Statistical methods for assessing agreement between two methods of clinical measurement. Lancet 1:8476 (1986), 307–310.
-
(1986)
Lancet
, vol.1
, Issue.8476
, pp. 307-310
-
-
Bland, J.M.1
Altman, D.G.2
-
37
-
-
84924907585
-
Anonymous effects of forced expiratory maneuvers and bronchodilator on lung clearance index in infants
-
37 Brown, M., Jensen, R., Balkovec, S., et al. Anonymous effects of forced expiratory maneuvers and bronchodilator on lung clearance index in infants. Am J Respir Crit Care Med, 183, 2011, A6311.
-
(2011)
Am J Respir Crit Care Med
, vol.183
, pp. A6311
-
-
Brown, M.1
Jensen, R.2
Balkovec, S.3
-
38
-
-
77449097660
-
Short-term effect of physiotherapy on variability of the lung clearance index in children with cystic fibrosis
-
38 Fuchs, S.I., Toussaint, S., Edlhaimb, B., Ballmann, M., Gappa, M., Short-term effect of physiotherapy on variability of the lung clearance index in children with cystic fibrosis. Pediatr Pulmonol 45:3 (2010), 301–306.
-
(2010)
Pediatr Pulmonol
, vol.45
, Issue.3
, pp. 301-306
-
-
Fuchs, S.I.1
Toussaint, S.2
Edlhaimb, B.3
Ballmann, M.4
Gappa, M.5
-
39
-
-
81455154503
-
Long-term course of lung clearance index between infancy and school-age in cystic fibrosis subjects
-
39 Kieninger, E., Singer, F., Fuchs, O., et al. Long-term course of lung clearance index between infancy and school-age in cystic fibrosis subjects. J Cyst Fibros 10:6 (2011), 487–490.
-
(2011)
J Cyst Fibros
, vol.10
, Issue.6
, pp. 487-490
-
-
Kieninger, E.1
Singer, F.2
Fuchs, O.3
-
40
-
-
84948971137
-
Progressive ventilation inhomogeneity in infants with cystic fibrosis after pulmonary infection
-
40 Simpson, S.J., Ranganathan, S., Park, J., et al. Progressive ventilation inhomogeneity in infants with cystic fibrosis after pulmonary infection. Eur Respir J 46:6 (2015), 1680–1690.
-
(2015)
Eur Respir J
, vol.46
, Issue.6
, pp. 1680-1690
-
-
Simpson, S.J.1
Ranganathan, S.2
Park, J.3
-
41
-
-
84884683771
-
Evolution of lung function during the first year of life in newborn screened cystic fibrosis infants
-
41 Nguyen, T.T., Thia, L.P., Hoo, A.F., et al. Evolution of lung function during the first year of life in newborn screened cystic fibrosis infants. Thorax 69:10 (2014), 910–917.
-
(2014)
Thorax
, vol.69
, Issue.10
, pp. 910-917
-
-
Nguyen, T.T.1
Thia, L.P.2
Hoo, A.F.3
-
42
-
-
84882899722
-
Treatment complexity in cystic fibrosis: trends over time and associations with site-specific outcomes
-
42 Sawicki, G.S., Ren, C.L., Konstan, M.W., et al. Treatment complexity in cystic fibrosis: trends over time and associations with site-specific outcomes. J Cyst Fibros 12:5 (2013), 461–467.
-
(2013)
J Cyst Fibros
, vol.12
, Issue.5
, pp. 461-467
-
-
Sawicki, G.S.1
Ren, C.L.2
Konstan, M.W.3
-
43
-
-
27144479427
-
Development and validation of the Cystic Fibrosis Questionnaire in the United States: a health-related quality-of-life measure for cystic fibrosis
-
43 Quittner, A.L., Buu, A., Messer, M.A., Modi, A.C., Watrous, M., Development and validation of the Cystic Fibrosis Questionnaire in the United States: a health-related quality-of-life measure for cystic fibrosis. Chest 128:4 (2005), 2347–2354.
-
(2005)
Chest
, vol.128
, Issue.4
, pp. 2347-2354
-
-
Quittner, A.L.1
Buu, A.2
Messer, M.A.3
Modi, A.C.4
Watrous, M.5
-
44
-
-
84860477440
-
A realistic validation study of a new nitrogen multiple-breath washout system
-
44 Singer, F., Houltz, B., Latzin, P., Robinson, P., Gustafsson, P., A realistic validation study of a new nitrogen multiple-breath washout system. PLoS One, 7(4), 2012, e36083.
-
(2012)
PLoS One
, vol.7
, Issue.4
, pp. e36083
-
-
Singer, F.1
Houltz, B.2
Latzin, P.3
Robinson, P.4
Gustafsson, P.5
|