Cystic fibrosis and survival to 40 years: A study of cystic fibrosis transmembrane conductance regulator function

European Respiratory Journal

Volumn 37, Issue 5, 2011, Pages 1076-1082

  Simmonds, N J ^a   D'Souza, L ^a   Roughton, M ^a   Alton, E W F W ^b   Davies, J C ^a   Hodson, M E ^a  

^a ROYAL BROMPTON HOSPITAL   (United Kingdom)

^b NATIONAL HEART AND LUNG INSTITUTE   (United Kingdom)

Author keywords

Cystic fibrosis; Forced expiratory volume in 1 s; Nasal potential difference; Survival; Sweat chloride

Indexed keywords

AMILORIDE; CHLORIDE; TRANSMEMBRANE CONDUCTANCE REGULATOR;

ADULT; AGE DISTRIBUTION; ARTICLE; CHLORIDE TRANSPORT; CONTROLLED STUDY; CYSTIC FIBROSIS; DISEASE SEVERITY; FEMALE; FORCED EXPIRATORY VOLUME; FORCED VITAL CAPACITY; FUNCTIONAL RESIDUAL CAPACITY; GENE MUTATION; HUMAN; MAJOR CLINICAL STUDY; MALE; OVERALL SURVIVAL; POTENTIAL DIFFERENCE; PRIORITY JOURNAL; PROSPECTIVE STUDY; PROTEIN FUNCTION; SEX RATIO; SURVIVAL TIME; SURVIVOR;

ADOLESCENT; ADULT; CYSTIC FIBROSIS; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; FEMALE; HUMANS; MALE; MEMBRANE POTENTIALS; MIDDLE AGED; MUTATION; NASAL MUCOSA; PROSPECTIVE STUDIES; RESPIRATORY FUNCTION TESTS; SEVERITY OF ILLNESS INDEX; SURVIVORS; SWEAT; YOUNG ADULT;

EID: 79955644127     PISSN: 09031936     EISSN: 13993003     Source Type: Journal    
DOI: 10.1183/09031936.00079010     Document Type: Article

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