RAN Translation in Huntington Disease

Neuron

Volumn 88, Issue 4, 2015, Pages 667-677

  Bañez Coronel, Monica ^a   Ayhan, Fatma ^a   Tarabochia, Alex D ^a   Zu, Tao ^a   Perez, Barbara A ^a   Tusi, Solaleh Khoramian ^a   Pletnikova, Olga ^c   Borchelt, David R ^a,b   Ross, Christopher A ^c   Margolis, Russell L ^c   Yachnis, Anthony T ^b   Troncoso, Juan C ^c   Ranum, Laura P W ^a  

^a UNIVERSITY OF FLORIDA   (United States)

^b UNIVERSITY OF FLORIDA COLLEGE OF MEDICINE   (United States)

^c JOHNS HOPKINS UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

POLYALANINE; POLYCYSTEINE; POLYLEUCINE; POLYPEPTIDE; POLYSERINE; RAN PROTEIN; UNCLASSIFIED DRUG; COMPLEMENTARY RNA; HTT PROTEIN, HUMAN; HUNTINGTIN; NERVE PROTEIN; PEPTIDE; POLYGLUTAMINE;

ADULT; AGED; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; APOPTOSIS; ARTICLE; BIOACCUMULATION; CAUDATE NUCLEUS; CELL SURVIVAL; CEREBELLUM; CHILD; CLINICAL ARTICLE; CONTROLLED STUDY; CORPUS STRIATUM; EMBRYO; FEMALE; FRONTAL CORTEX; GENE MUTATION; HUMAN; HUMAN CELL; HUMAN TISSUE; HUNTINGTON CHOREA; IN VITRO STUDY; IN VIVO STUDY; MALE; MICROGLIA; MIDDLE AGED; MOUSE; NERVE CELL NECROSIS; NERVOUS SYSTEM INFLAMMATION; NONHUMAN; OPEN READING FRAME; PRESCHOOL CHILD; PRIORITY JOURNAL; PROTEIN AGGREGATION; PROTEIN EXPRESSION; PUTAMEN; RNA TRANSLATION; VERY ELDERLY; WHITE MATTER; YOUNG ADULT; BRAIN; CASE CONTROL STUDY; FRONTAL LOBE; GENETICS; HEK293 CELL LINE; METABOLISM; NEOSTRIATUM; PROTEIN SYNTHESIS; PROTEINOSIS; TRINUCLEOTIDE REPEAT;

ADULT; AGED, 80 AND OVER; BRAIN; CASE-CONTROL STUDIES; CEREBELLUM; CHILD; FEMALE; FRONTAL LOBE; HEK293 CELLS; HUMANS; HUNTINGTIN PROTEIN; HUNTINGTON DISEASE; MALE; MIDDLE AGED; NEOSTRIATUM; NERVE TISSUE PROTEINS; PEPTIDES; PROTEIN AGGREGATION, PATHOLOGICAL; PROTEIN BIOSYNTHESIS; RNA, ANTISENSE; TRINUCLEOTIDE REPEAT EXPANSION; YOUNG ADULT;

EID: 84959360025     PISSN: 08966273     EISSN: 10974199     Source Type: Journal    
DOI: 10.1016/j.neuron.2015.10.038     Document Type: Article

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