-
1
-
-
79952522208
-
Improved survival at low lung function in cystic fibrosis: Cohort study from 1990 to 2007
-
George PM, Banya W, Pareek N, et al. Improved survival at low lung function in cystic fibrosis: cohort study from 1990 to 2007. BMJ 2011; 342: d1008.
-
(2011)
BMJ
, vol.342
, pp. d1008
-
-
George, P.M.1
Banya, W.2
Pareek, N.3
-
2
-
-
84878119352
-
Ageing in cystic fibrosis and long-term survival
-
Simmonds NJ. Ageing in cystic fibrosis and long-term survival. Paediatr Respir Rev 2013; 14: Suppl. 1, 6-9.
-
(2013)
Paediatr Respir Rev
, vol.14
, pp. 6-9
-
-
Simmonds, N.J.1
-
3
-
-
79953305852
-
Changing epidemiology and clinical issues arising in an ageing cystic fibrosis population
-
Parkins MD, Parkins VM, Rendall JC, et al. Changing epidemiology and clinical issues arising in an ageing cystic fibrosis population. Ther Adv Respir Dis 2011; 5: 105-119.
-
(2011)
Ther Adv Respir Dis
, vol.5
, pp. 105-119
-
-
Parkins, M.D.1
Parkins, V.M.2
Rendall, J.C.3
-
4
-
-
54049139978
-
Persistent methicillin-resistant Staphylococcus aureus and rate of FEV1 decline in cystic fibrosis
-
Dasenbrook EC, Merlo CA, Diener-West M, et al. Persistent methicillin-resistant Staphylococcus aureus and rate of FEV1 decline in cystic fibrosis. Am J Respir Crit Care Med 2008; 178: 814-821.
-
(2008)
Am J Respir Crit Care Med
, vol.178
, pp. 814-821
-
-
Dasenbrook, E.C.1
Merlo, C.A.2
Diener-West, M.3
-
5
-
-
77953635880
-
Association between respiratory tract methicillin-resistant Staphylococcus aureus and survival in cystic fibrosis
-
Dasenbrook EC, Checkley W, Merlo CA, et al. Association between respiratory tract methicillin-resistant Staphylococcus aureus and survival in cystic fibrosis. JAMA 2010; 303: 2386-2392.
-
(2010)
JAMA
, vol.303
, pp. 2386-2392
-
-
Dasenbrook, E.C.1
Checkley, W.2
Merlo, C.A.3
-
6
-
-
76749131586
-
Patient segregation and aggressive antibiotic eradication therapy can control methicillin-resistant Staphylococcus aureus at large cystic fibrosis centres
-
Doe SJ, McSorley A, Isalska B, et al. Patient segregation and aggressive antibiotic eradication therapy can control methicillin-resistant Staphylococcus aureus at large cystic fibrosis centres. J Cyst Fibros 2010; 9: 104-109.
-
(2010)
J Cyst Fibros
, vol.9
, pp. 104-109
-
-
Doe, S.J.1
McSorley, A.2
Isalska, B.3
-
8
-
-
84901016914
-
European cystic fibrosis society standards of care: Framework for the cystic fibrosis centre
-
Conway S, Balfour-Lynn IM, De Rijcke K, et al. European Cystic Fibrosis Society Standards of Care: Framework for the Cystic Fibrosis Centre. J Cyst Fibros 2014; 13: Suppl. 1, S3-S22.
-
(2014)
J Cyst Fibros
, vol.13
, pp. S3-S22
-
-
Conway, S.1
Balfour-Lynn, I.M.2
De Rijcke, K.3
-
9
-
-
78649759755
-
Cystic fibrosis and survival to 40 years: A case-control study
-
Simmonds NJ, Macneill SJ, Cullinan P, et al. Cystic fibrosis and survival to 40 years: a case-control study. Eur Respir J 2010; 36: 1277-1283.
-
(2010)
Eur Respir J
, vol.36
, pp. 1277-1283
-
-
Simmonds, N.J.1
Macneill, S.J.2
Cullinan, P.3
-
10
-
-
84937406021
-
Future trends in cystic fibrosis demography in 34 European countries
-
Burgel PR, Bellis G, Olesen H, et al. Future trends in cystic fibrosis demography in 34 European countries. Eur Respir J 2015; 46: 133-141.
-
(2015)
Eur Respir J
, vol.46
, pp. 133-141
-
-
Burgel, P.R.1
Bellis, G.2
Olesen, H.3
-
11
-
-
84918774941
-
Long-term safety and efficacy of ivacaftor in patients with cystic fibrosis who have the Gly551Asp-CFTR mutation: A phase 3, open-label extension study (PERSIST)
-
McKone EF, Borowitz D, Drevinek P, et al. Long-term safety and efficacy of ivacaftor in patients with cystic fibrosis who have the Gly551Asp-CFTR mutation: a phase 3, open-label extension study (PERSIST). Lancet Respir Med 2014; 11 902-910.
-
(2014)
Lancet Respir Med
, vol.11
, pp. 902-910
-
-
McKone, E.F.1
Borowitz, D.2
Drevinek, P.3
-
12
-
-
84911493956
-
Efficacy and safety of ivacaftor in patients with cystic fibrosis and a non-G551D gating mutation
-
De Boeck K, Munck A, Walker S, et al. Efficacy and safety of ivacaftor in patients with cystic fibrosis and a non-G551D gating mutation. J Cyst Fibros 2014; 13 674-680.
-
(2014)
J Cyst Fibros
, vol.13
, pp. 674-680
-
-
De Boeck, K.1
Munck, A.2
Walker, S.3
-
13
-
-
84907054376
-
Ivacaftor for patients with cystic fibrosis
-
Wainwright CE. Ivacaftor for patients with cystic fibrosis. Expert Rev Respir Med 2014; 8: 533-538.
-
(2014)
Expert Rev Respir Med
, vol.8
, pp. 533-538
-
-
Wainwright, C.E.1
-
14
-
-
80455162465
-
A CFTR potentiator in patients with cystic fibrosis and the G551D mutation
-
Ramsey BW, Davies J, McElvaney NG, et al. A CFTR potentiator in patients with cystic fibrosis and the G551D mutation. N Engl J Med 2011; 365: 1663-1672.
-
(2011)
N Engl J Med
, vol.365
, pp. 1663-1672
-
-
Ramsey, B.W.1
Davies, J.2
McElvaney, N.G.3
-
15
-
-
84880030599
-
Management of comorbidities in older patients with cystic fibrosis
-
Plant BJ, Goss CH, Plant WD, et al. Management of comorbidities in older patients with cystic fibrosis. Lancet Respir Med 2013; 1: 164-174.
-
(2013)
Lancet Respir Med
, vol.1
, pp. 164-174
-
-
Plant, B.J.1
Goss, C.H.2
Plant, W.D.3
-
16
-
-
84895069466
-
Hypersensitivity to antibiotics in patients with cystic fibrosis
-
Roehmel JF, Schwarz C, Mehl A, et al. Hypersensitivity to antibiotics in patients with cystic fibrosis. J Cyst Fibros 2014; 13: 205-211.
-
(2014)
J Cyst Fibros
, vol.13
, pp. 205-211
-
-
Roehmel, J.F.1
Schwarz, C.2
Mehl, A.3
-
17
-
-
84907257157
-
Increased risk of colorectal neoplasia in adult patients with cystic fibrosis: A matched case-control study
-
Gory I, Brown G, Wilson J, et al. Increased risk of colorectal neoplasia in adult patients with cystic fibrosis: a matched case-control study. Scand J Gastroenterol 2014; 49: 1230-1236.
-
(2014)
Scand J Gastroenterol
, vol.49
, pp. 1230-1236
-
-
Gory, I.1
Brown, G.2
Wilson, J.3
-
18
-
-
84872557485
-
Cancer risk in cystic fibrosis: A 20-year nationwide study from the United States
-
Maisonneuve P, Marshall BC, Knapp EA, et al. Cancer risk in cystic fibrosis: a 20-year nationwide study from the United States. J Natl Cancer Inst 2013; 105: 122-129.
-
(2013)
J Natl Cancer Inst
, vol.105
, pp. 122-129
-
-
Maisonneuve, P.1
Marshall, B.C.2
Knapp, E.A.3
-
19
-
-
84922750157
-
Overweight and obesity in patients with cystic fibrosis: A center-based analysis
-
Hanna RM, Weiner DJ. Overweight and obesity in patients with cystic fibrosis: a center-based analysis. Pediatr Pulmonol 2015; 50: 35-44.
-
(2015)
Pediatr Pulmonol
, vol.50
, pp. 35-44
-
-
Hanna, R.M.1
Weiner, D.J.2
-
20
-
-
84861892787
-
Increased arterial stiffness in children with cystic fibrosis
-
Buehler T, Steinmann M, Singer F, et al. Increased arterial stiffness in children with cystic fibrosis. Eur Respir J 2012; 39: 1536-1537.
-
(2012)
Eur Respir J
, vol.39
, pp. 1536-1537
-
-
Buehler, T.1
Steinmann, M.2
Singer, F.3
-
21
-
-
84901006449
-
European Cystic Fibrosis Society Standards of Care: Best Practice guidelines
-
Smyth AR, Bell SC, Bojcin S, et al. European Cystic Fibrosis Society Standards of Care: Best Practice guidelines. J Cyst Fibros 2014; 13: Suppl. 1, S23-S42.
-
(2014)
J Cyst Fibros
, vol.13
, pp. S23-S42
-
-
Smyth, A.R.1
Bell, S.C.2
Bojcin, S.3
-
22
-
-
84901058087
-
European Cystic Fibrosis Society Standards of Care: Quality Management in cystic fibrosis
-
Stern M, Bertrand DP, Bignamini E, et al. European Cystic Fibrosis Society Standards of Care: Quality Management in cystic fibrosis. J Cyst Fibros 2014; 13: Suppl. 1, S43-S59.
-
(2014)
J Cyst Fibros
, vol.13
, pp. S43-S59
-
-
Stern, M.1
Bertrand, D.P.2
Bignamini, E.3
-
23
-
-
84887043778
-
Health outcomes associated with transition from pediatric to adult cystic fibrosis care
-
Tuchman L, Schwartz M. Health outcomes associated with transition from pediatric to adult cystic fibrosis care. Pediatrics 2013; 132: 847.
-
(2013)
Pediatrics
, vol.132
, pp. 847
-
-
Tuchman, L.1
Schwartz, M.2
-
24
-
-
0034296410
-
Cystic fibrosis in adolescents and young adults
-
Nasr SZ. Cystic fibrosis in adolescents and young adults. Adolesc Med 2000; 11: 589-603.
-
(2000)
Adolesc Med
, vol.11
, pp. 589-603
-
-
Nasr, S.Z.1
-
26
-
-
84926198675
-
Adherence of subjects with cystic fibrosis to their home program: A systematic review
-
O'Donohoe R, Fullen BM. Adherence of subjects with cystic fibrosis to their home program: a systematic review. Respir Care 2014; 59: 1731-1746.
-
(2014)
Respir Care
, vol.59
, pp. 1731-1746
-
-
O'Donohoe, R.1
Fullen, B.M.2
-
27
-
-
84920941168
-
Motivating adherence among adolescents with cystic fibrosis: Youth and parent perspectives
-
Sawicki GS, Heller KS, Demars N, et al. Motivating adherence among adolescents with cystic fibrosis: youth and parent perspectives. Pediatr Pulmonol 2015; 50: 127-136.
-
(2015)
Pediatr Pulmonol
, vol.50
, pp. 127-136
-
-
Sawicki, G.S.1
Heller, K.S.2
Demars, N.3
-
28
-
-
84919721435
-
Prevalence of depression and anxiety in patients with cystic fibrosis and parent caregivers: Results of the International Depression Epidemiological Study across nine countries
-
Quittner AL, Goldbeck L, Abbott J, et al. Prevalence of depression and anxiety in patients with cystic fibrosis and parent caregivers: results of The International Depression Epidemiological Study across nine countries. Thorax 2014; 69: 1090-1097.
-
(2014)
Thorax
, vol.69
, pp. 1090-1097
-
-
Quittner, A.L.1
Goldbeck, L.2
Abbott, J.3
-
30
-
-
79957946294
-
Managing cystic fibrosis: Strategies that increase life expectancy and improve quality of life
-
Cohen-Cymberknoh M, Shoseyov D, Kerem E. Managing cystic fibrosis: strategies that increase life expectancy and improve quality of life. Am J Respir Crit Care Med 2011; 183: 1463-1471.
-
(2011)
Am J Respir Crit Care Med
, vol.183
, pp. 1463-1471
-
-
Cohen-Cymberknoh, M.1
Shoseyov, D.2
Kerem, E.3
-
31
-
-
84882899722
-
Treatment complexity in cystic fibrosis: Trends over time and associations with site-specific outcomes
-
Sawicki GS, Ren CL, Konstan MW, et al. Treatment complexity in cystic fibrosis: trends over time and associations with site-specific outcomes. J Cyst Fibros 2013; 12: 461-467.
-
(2013)
J Cyst Fibros
, vol.12
, pp. 461-467
-
-
Sawicki, G.S.1
Ren, C.L.2
Konstan, M.W.3
-
32
-
-
84903298392
-
Pulmonary medication adherence and health-care use in cystic fibrosis
-
Quittner AL, Zhang J, Marynchenko M, et al. Pulmonary medication adherence and health-care use in cystic fibrosis. Chest 2014; 146: 142-151.
-
(2014)
Chest
, vol.146
, pp. 142-151
-
-
Quittner, A.L.1
Zhang, J.2
Marynchenko, M.3
-
33
-
-
77449104871
-
Motivational interviewing for adherence problems in cystic fibrosis
-
Duff AJ, Latchford GJ. Motivational interviewing for adherence problems in cystic fibrosis. Pediatr Pulmonol 2010; 45: 211-220.
-
(2010)
Pediatr Pulmonol
, vol.45
, pp. 211-220
-
-
Duff, A.J.1
Latchford, G.J.2
-
34
-
-
84924339670
-
Screening and assessment: Psycological intervention, pharmacologicial interventions
-
Smith B, Goldbeck L, Georgiopoulos AM. Screening and assessment: psycological intervention, pharmacologicial interventions. Ped Pulmonol 2014; 49: 171-172.
-
(2014)
Ped Pulmonol
, vol.49
, pp. 171-172
-
-
Smith, B.1
Goldbeck, L.2
Georgiopoulos, A.M.3
-
36
-
-
84905751263
-
Psychological interventions for individuals with cystic fibrosis and their families
-
Goldbeck L, Fidika A, Herle M, et al. Psychological interventions for individuals with cystic fibrosis and their families. Cochrane Database Syst Rev 2014; 6: CD003148.
-
(2014)
Cochrane Database Syst Rev
, vol.6
, pp. CD003148
-
-
Goldbeck, L.1
Fidika, A.2
Herle, M.3
-
37
-
-
84884326788
-
Longitudinal trends in health-related quality of life in adults with cystic fibrosis
-
Dill EJ, Dawson R, Sellers DE, et al. Longitudinal trends in health-related quality of life in adults with cystic fibrosis. Chest 2013; 144: 981-989.
-
(2013)
Chest
, vol.144
, pp. 981-989
-
-
Dill, E.J.1
Dawson, R.2
Sellers, D.E.3
-
38
-
-
84872070847
-
Atypical cystic fibrosis: Identification in the primary care setting
-
Schram CA. Atypical cystic fibrosis: identification in the primary care setting. Can Fam Physician 2012; 58: 1341-1345.
-
(2012)
Can Fam Physician
, vol.58
, pp. 1341-1345
-
-
Schram, C.A.1
-
39
-
-
79958122789
-
Recommendations for the classification of diseases as CFTR-related disorders
-
Bombieri C, Claustres M, De Boeck K, et al. Recommendations for the classification of diseases as CFTR-related disorders. J Cyst Fibros 2011; 10: Suppl. 2, S86-102.
-
(2011)
J Cyst Fibros
, vol.10
, pp. S86-102
-
-
Bombieri, C.1
Claustres, M.2
De Boeck, K.3
-
40
-
-
84879961930
-
Lung transplantation for cystic fibrosis and bronchiectasis
-
Corris PA. Lung transplantation for cystic fibrosis and bronchiectasis. Semin Respir Crit Care Med 2013; 34: 297-304.
-
(2013)
Semin Respir Crit Care Med
, vol.34
, pp. 297-304
-
-
Corris, P.A.1
-
41
-
-
0037115262
-
Developing cystic fibrosis lung transplant referral criteria using predictors of 2-year mortality
-
Mayer-Hamblett N, Rosenfeld M, Emerson J, et al. Developing cystic fibrosis lung transplant referral criteria using predictors of 2-year mortality. Am J Respir Crit Care Med 2002; 166: 1550-1555.
-
(2002)
Am J Respir Crit Care Med
, vol.166
, pp. 1550-1555
-
-
Mayer-Hamblett, N.1
Rosenfeld, M.2
Emerson, J.3
-
43
-
-
83755171696
-
Clinical review: Extracorporeal membrane oxygenation
-
Gattinoni L, Carlesso E, Langer T. Clinical review: extracorporeal membrane oxygenation. Crit Care 2011; 15: 243.
-
(2011)
Crit Care
, vol.15
, pp. 243
-
-
Gattinoni, L.1
Carlesso, E.2
Langer, T.3
-
44
-
-
84899501409
-
Practical guidelines: Lung transplantation in patients with cystic fibrosis
-
Hirche TO, Knoop C, Hebestreit H, et al. Practical guidelines: lung transplantation in patients with cystic fibrosis. Pulm Med 2014; 2014: 621342.
-
(2014)
Pulm Med
, vol.2014
, pp. 621342
-
-
Hirche, T.O.1
Knoop, C.2
Hebestreit, H.3
-
45
-
-
79958271457
-
End of life care in CF: Patients, families and staff experiences and unmet needs
-
Braithwaite M, Philip J, Tranberg H, et al. End of life care in CF: patients, families and staff experiences and unmet needs. J Cyst Fibros 2011; 10: 253-257.
-
(2011)
J Cyst Fibros
, vol.10
, pp. 253-257
-
-
Braithwaite, M.1
Philip, J.2
Tranberg, H.3
-
46
-
-
79958134733
-
End of life care for patients with cystic fibrosis
-
Sands D, Repetto T, Dupont LJ, et al. End of life care for patients with cystic fibrosis. J Cyst Fibros 2011; 10: S37-S44.
-
(2011)
J Cyst Fibros
, vol.10
, pp. S37-S44
-
-
Sands, D.1
Repetto, T.2
Dupont, L.J.3
-
47
-
-
84882889658
-
Self-efficacy: Empowering parents of children with cystic fibrosis
-
McDonald CM, Haberman D, Brown N. Self-efficacy: empowering parents of children with cystic fibrosis. J Cyst Fibros 2013; 12: 538-543.
-
(2013)
J Cyst Fibros
, vol.12
, pp. 538-543
-
-
McDonald, C.M.1
Haberman, D.2
Brown, N.3
-
48
-
-
84882948337
-
A longitudinal study of the impact of social deprivation and disease severity on employment status in the UK cystic fibrosis population
-
Taylor-Robinson DC, Smyth R, Diggle PJ, et al. A longitudinal study of the impact of social deprivation and disease severity on employment status in the UK cystic fibrosis population. PLoS One 2013; 8: e73322.
-
(2013)
PLoS One
, vol.8
, pp. e73322
-
-
Taylor-Robinson, D.C.1
Smyth, R.2
Diggle, P.J.3
-
50
-
-
0036674744
-
A model for transition from pediatric to adult care of care in cystic fibrosis
-
Madge S, Bryon M. A model for transition from pediatric to adult care of care in cystic fibrosis. J Pediatr Nurs 2002; 17: 283-288.
-
(2002)
J Pediatr Nurs
, vol.17
, pp. 283-288
-
-
Madge, S.1
Bryon, M.2
-
51
-
-
0345963017
-
Transition programs in cystic fibrosis centers: Perceptions of team members
-
Flume PA, Taylor LA, Anderson DL, et al. Transition programs in cystic fibrosis centers: perceptions of team members. Pediatr Pulmonol 2004; 37: 4-7.
-
(2004)
Pediatr Pulmonol
, vol.37
, pp. 4-7
-
-
Flume, P.A.1
Taylor, L.A.2
Anderson, D.L.3
-
52
-
-
84919846360
-
Determinants of respiratory pump function in patients with cystic fibrosis
-
Dassios T. Determinants of respiratory pump function in patients with cystic fibrosis. Paediatr Respir Rev 2015; 16: 75-79.
-
(2015)
Paediatr Respir Rev
, vol.16
, pp. 75-79
-
-
Dassios, T.1
-
53
-
-
84904424764
-
Infection prevention and control guideline for cystic fibrosis: 2013 update
-
Saiman L, Siegel JD, LiPuma JJ, et al. Infection prevention and control guideline for cystic fibrosis: 2013 update. Infect Control Hosp Epidemiol 2014; 35: Suppl. 1, S1-S67.
-
(2014)
Infect Control Hosp Epidemiol
, vol.35
, pp. S1-S67
-
-
Saiman, L.1
Siegel, J.D.2
LiPuma, J.J.3
-
54
-
-
84455209635
-
Full, shared and hybrid paediatric care for cystic fibrosis in South and Mid Wales
-
Doull I, Evans H, South and Mid Wales Paediatric Cystic Fibrosis Network. Full, shared and hybrid paediatric care for cystic fibrosis in South and Mid Wales. Arch Dis Child 2012; 97: 17-20.
-
(2012)
Arch Dis Child
, vol.97
, pp. 17-20
-
-
Doull, I.1
Evans, H.2
-
55
-
-
69549098338
-
Implementation of European standards of care for cystic fibrosis - Provision of care
-
Elborn JS, Hodson M, Bertram C. Implementation of European standards of care for cystic fibrosis - provision of care. J Cyst Fibros 2009; 8: 348-355.
-
(2009)
J Cyst Fibros
, vol.8
, pp. 348-355
-
-
Elborn, J.S.1
Hodson, M.2
Bertram, C.3
-
56
-
-
84885702043
-
Program of home telemonitoring in patients with cystic fibrosis over a period of 2 years: A contribution to the rationalization of care
-
Bella S, Murgia F, Cotognini C, et al. Program of home telemonitoring in patients with cystic fibrosis over a period of 2 years: a contribution to the rationalization of care. Clin Ter 2013; 164: e313-e317.
-
(2013)
Clin ter
, vol.164
, pp. e313-e317
-
-
Bella, S.1
Murgia, F.2
Cotognini, C.3
-
57
-
-
84857883363
-
Telehealth in cystic fibrosis: A systematic review
-
Cox NS, Alison JA, Rasekaba T, et al. Telehealth in cystic fibrosis: a systematic review. J Telemed Telecare 2012; 18: 72-78.
-
(2012)
J Telemed Telecare
, vol.18
, pp. 72-78
-
-
Cox, N.S.1
Alison, J.A.2
Rasekaba, T.3
-
58
-
-
84885702043
-
Program of home telemonitoring in patients with cystic fibrosis over a period of 2 years: A contribution to the rationalization of care
-
Bella S, Murgia F, Cotognini C, et al. Program of home telemonitoring in patients with cystic fibrosis over a period of 2 years: a contribution to the rationalization of care. Clin Ter 2013; 164: e313-e317.
-
(2013)
Clin ter
, vol.164
, pp. e313-e317
-
-
Bella, S.1
Murgia, F.2
Cotognini, C.3
-
59
-
-
84900614645
-
-
Harmonised Education in Respiratory Medicine for European Specialists. Accreditation process. http://hermes. ersnet.org/accreditation/accreditation-process/
-
Accreditation Process
-
-
|