Wolfram Syndrome: Diagnosis, Management, and Treatment

Current Diabetes Reports

Volumn 16, Issue 1, 2016, Pages 1-8

  Urano, Fumihiko ^a  

^a WASHINGTON UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

Blindness; Deafness; Endoplasmic reticulum stress; Genetic disorder; Neurodegeneration; Type 1 diabetes; Type 2 diabetes; Wolfram syndrome; cells

Indexed keywords

4 PHENYLBUTYRIC ACID; TAUROURSODEOXYCHOLIC ACID;

ATAXIA; AUTONOMIC NEUROPATHY; BRAIN ATROPHY; CANCER PROGNOSIS; CELL DAMAGE; CLINICAL ASSESSMENT; CLINICAL FEATURE; DIABETES INSIPIDUS; DISEASE COURSE; DISEASE SEVERITY; DRUG TARGETING; DYSPHAGIA; ENDOCRINE DISEASE; ENDOPLASMIC RETICULUM STRESS; EYE DISEASE; GENE THERAPY; GENETIC DISORDER; HEADACHE; HEARING IMPAIRMENT; HUMAN; HYPOGONADISM; HYPONATREMIA; INSULIN DEPENDENT DIABETES MELLITUS; MENTAL DISEASE; MOLECULAR PATHOLOGY; NERVE DEGENERATION; NEUROLOGIC DISEASE; NONHUMAN; OPTIC NERVE ATROPHY; PATIENT CARE; PATIENT MONITORING; PHYSICAL EXAMINATION; QUALITY OF LIFE; RARE DISEASE; REGENERATIVE MEDICINE; REVIEW; SYMPTOM; TARGET CELL DESTRUCTION; URINARY TRACT DISEASE; WOLFRAM SYNDROME; ANIMAL; COMPLICATION; NON INSULIN DEPENDENT DIABETES MELLITUS; PATHOPHYSIOLOGY; PROGNOSIS;

ANIMALS; DIABETES MELLITUS, TYPE 1; DIABETES MELLITUS, TYPE 2; DISEASE PROGRESSION; HUMANS; PROGNOSIS; QUALITY OF LIFE; WOLFRAM SYNDROME;

EID: 84953390394     PISSN: 15344827     EISSN: 15390829     Source Type: Journal    
DOI: 10.1007/s11892-015-0702-6     Document Type: Review

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